No abstract

Papillon-Lefevre Syndrome (PLS) is a rare inherited autosomal-recessive condition with one-third of the patients' showing consanguinity of the parents. Lesions are characterised by palmar-plantar hyperkeratosis and hyperhidrosis. Early onset of periodonditis, severe periodontal destruction in both primary and permanent dentitions, and calcification of the duramater form the three important features of this disease. Here, we present a case of a 14-year-old female who presented to the Department of Oral Medicine and Radiology with a complaint of mobility of the teeth since four months. Oral examination of the patient showed generalised mobility of the teeth. General physical examination of the patient showed dry scaly skin on dorsum of bilateral feet, hands, and knee. The patient had familial history positive for consanguinity. The patient was medically diagnosed as positive for PLS. The patients with PLS show combination of dermatological and dental lesions and it requires the dentist to assume a more prominent role in early treatment and rehabilitation. There is a need for symbiotic and synergetic approach between the two specialties for effective management of this rare disease.

ObjectivesThis systematic review evaluated whether CBCT is a better diagnostic tool in facial forensic reconstruction. Forensic facial reconstruction is a technique to reconstruct human face from unidentified face from skull remains for human identification and facial recognition.Materials and methodsArticle selection and data extraction was done based on the inclusion and exclusion criteria devised for the study. The articles were screened from PubMed, ProQuest, Google scholar, Science direct and Scopus.ResultThree hundred and thirty-nine articles were initially identified from which seven articles were full text reviewed and included in the review. All the articles included in this study suggest that the facial reconstruction done using CBCT are reliable. ConclusionThe computerized 3D modeling method produces reliable facial reconstructions which involves the images scanned from CBCT and the combination method. The computerized 3D modeling method produces facial reconstruction which almost mimics the original resemblance.

Amelogenesis imperfecta (AI) refers to a group of rare genetic disorders that involve tooth development and that are passed down through families as a dominant trait. This condition is characterized by abnormal enamel formation caused by gene mutations that alter the quality and/or quantity of enamel. This dental problem can impact both primary and permanent dentition, varies among affected individuals, and results in esthetic and functional problems. The treatment planning for patients with AI is related to many factors, including the age of the patient, the type and severity of the disorder, intraoral conditions, and the socioeconomic status of the patient. It is crucial to plan a proper remedy, which requires collaboration among dental specialties to execute comprehensive dental treatment in order to provide a long-term solution with adequate esthetics. This clinical case study looks at three different types of amelogenesis imperfecta patients.