Unguarded tricuspid orifice and patent right ventricular outflow tract presenting with long-standing severe right heart failure in an adult

Congenitally unguarded tricuspid valve orifice with a hypoplastic right ventricle and free thrombus in a giant right atrium

“…An isolated unguarded tricuspid orifice with no other congenital abnormality has been reported in few cases so far 1,[3][4][5]9 . No case of an asymtomatic patient surviving till adulthood has been reported.…”

“…Publications reporting ante-mortem diagnosis of congenitally unguarded tricuspid valve orifice, a rare condition are limited in number [1][2][3][4][5] . An isolated unguarded tricuspid orifice with no other congenital abnormality has been reported in few cases so far 1,[3][4][5]9 .…”

“…Primary tricuspid valve disease related to congenital malformation of the tricuspid valve other than Ebstein's anomaly is rare, with description in few ante-mortem case reports [1][2][3][4][5] . It is a variant of tricuspid valve dysplasia where-in there is partial or complete agenesis of tricuspid valve tissue.…”

Isolated unguarded tricuspid valve: A rare cause of syncope and new-onset right cardiac failure in adult

“…An unguarded tricuspid valve is a rare congenital anomaly described in only a few antemortem case reports [1][2][3][4][5][6][7][8][9][10][11][12]. It is a variant of tricuspid valve dysplasia wherein there is partial or complete agenesis of tricuspid valve tissue [2].…”

“…The clinical presentation is usually in early childhood with cyanosis and/or congestive heart failure but there are a few patients in whom decompensation occurs during adult life with right ventricular failure and tricuspid regurgitation [8][9][10]. Rarely, an unguarded tricuspid valve presents as an accidental finding in asymptomatic patient, who was evaluated by echocardiography for other reasons [11].…”