“…Congenitally unguarded tricuspid orifice with patent right ventricular outflow tract is a rare anomaly with <50 cases reported in the literature with antemortem diagnosis 1, 2, 3, 4, 5, 6, 7, 8, 9, 10, 11. Isolated unguarded tricuspid orifice with no other congenital abnormality has been reported in a few patients so far 1, 8, 9, 10.…”
Section: Discussionmentioning
confidence: 99%
“…Unguarded tricuspid valve (TV) with well-developed right ventricle (RV) and the patent outflow tract constitute a rare congenital anomaly with a few antemortem case reports 1, 2, 3, 4, 5, 6, 7, 8, 9, 10, 11. It is a variety of TV dysplasia, in which there is partial or complete agenesis of the TV tissue 12 .…”
Congenitally unguarded tricuspid valve (TV) orifice, a variant of TV dysplasia, is a rare malformation with protean manifestations. This report describes a symptomatic adult male with gross right heart failure and atrial fibrillation, who was found to have an unguarded TV orifice with isolation of the trabecular apical cavity of the right ventricle (RV) and muscular ridges separating outflow tract (forme-fruste of the double-chambered RV). The right ventricular outflow tract remained patent.
“…Congenitally unguarded tricuspid orifice with patent right ventricular outflow tract is a rare anomaly with <50 cases reported in the literature with antemortem diagnosis 1, 2, 3, 4, 5, 6, 7, 8, 9, 10, 11. Isolated unguarded tricuspid orifice with no other congenital abnormality has been reported in a few patients so far 1, 8, 9, 10.…”
Section: Discussionmentioning
confidence: 99%
“…Unguarded tricuspid valve (TV) with well-developed right ventricle (RV) and the patent outflow tract constitute a rare congenital anomaly with a few antemortem case reports 1, 2, 3, 4, 5, 6, 7, 8, 9, 10, 11. It is a variety of TV dysplasia, in which there is partial or complete agenesis of the TV tissue 12 .…”
Congenitally unguarded tricuspid valve (TV) orifice, a variant of TV dysplasia, is a rare malformation with protean manifestations. This report describes a symptomatic adult male with gross right heart failure and atrial fibrillation, who was found to have an unguarded TV orifice with isolation of the trabecular apical cavity of the right ventricle (RV) and muscular ridges separating outflow tract (forme-fruste of the double-chambered RV). The right ventricular outflow tract remained patent.
“…Other clinical presentations have also been reported, including arrhythmias and thrombosis . Patients with partial isolated unguarded TV, good RV function, and new‐onset right cardiac failure might benefit from tricuspid annuloplasty . However, in view of the frequent association with RV dysfunction, it does not seem to be an optimum long‐term option .…”
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