Tumores cardíacos primarios en la infancia

Andrés, Antonio Sánchez; Albert, B. Insa; Moreno, J.L. Pontones; Sánchez, Amaury Flores; Bonora, A. Moya; Palacios, J.M. Sáez

doi:10.1157/13124213

Cited by 13 publications

(12 citation statements)

References 14 publications

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“…Large tumors can cause an obstruction in the outflow or inflow tracts, and small ones can affect the conduction system causing dysrhythmias. [ 1 3 ] In this case, we are reporting a single rhabdomyoma located in an atypical location, near the crista terminalis, and diagnosed due to frequent supraventricular extrasystoles, the appearance of which preceded the capability of echocardiography to identify the tumor.…”

Section: Discussionmentioning

confidence: 99%

Neonatal supraventricular extrasystole as early clinical debut of cardiac rhabdomyoma

et al. 2018

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We are reporting the case of a newborn with a diagnosis of frequent supraventricular extrasystoles, up to 25% of beats at Holter monitoring, and partial response to beta-blockers. Initial echocardiographic studies were normal until the identification of a right atrial mass at 4 months of life. Given the progressive growth of the mass and the suspicion of myxoma or thrombus in the magnetic resonance study, surgical resection of the tumor was performed. The surgical specimen was histologically diagnostic of rhabdomyoma. Currently, the patient remains asymptomatic after a 6-year follow-up period. A single rhabdomyoma is described, located in an atypical situation, near the crista terminalis, and diagnosed from frequent extrasystoles which appeared before the echocardiographic resolution was able to identify it. Magnetic resonance showed nondiagnostic tissue enhancement characteristics.

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Section: Discussionmentioning

confidence: 99%

Neonatal supraventricular extrasystole as early clinical debut of cardiac rhabdomyoma

et al. 2018

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“…The most common variant in the pediatric population is rhabdomyoma (45-70%) and 60% of these cases are in patients with tuberous sclerosis. The next most frequently encountered primary tumors include fibromas (6-25%), teratomas (2-10%), vascular tumors, myxomas, and finally the pericardial teratoma, which comprises a minor percentage (1).…”

Section: Discussionmentioning

confidence: 99%

“…The clinical presentation is related to the size and location of the tumor. The signs and symptoms encountered occur in the following frequency: asymptomatic (63%), murmur (10%), arrhythmias (9%), seizures (5%), cyanosis, respiratory distress and cardiac insufficiency (4%), family history of tuberous sclerosis (3%), hydrops fetalis (2%), polyhydramnios (1%), and cerebral embolism (0.9%) (1-4).…”

Section: Discussionmentioning

confidence: 99%

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Primary Cardiac Tumors in Infancy: A Case Report and Literature Review

Domínguez

Perkins

Duque³

et al. 2017

Academic Forensic Pathology

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Sudden death in infants due to primary cardiac tumors is extremely rare. Herein we describe a case of an 8-month-old male infant, without any previous medical history, who died in a hospital in the city of Medellín-Antioquia, Colombia. The family stated that approximately 15 minutes after he received a bottle, the baby became cyanotic and subsequently lost consciousness. He was taken to the hospital immediately; however, he arrived lifeless. As this was a sudden death case, the child was referred to the Institute of Legal Medicine and Forensic Sciences in the city of Medellín to clarify the cause, manner, and mechanism of death. The forensic autopsy revealed a eutrophic infant with central and peripheral cyanosis, without signs of trauma, and the internal examination found a single cardiac tumor in the anterior wall of the left ventricle. The mass was white and whorled; histological evaluation diagnosed a fibroma. The manner of death was natural due to a cardiogenic shock caused by a primary tumor.

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“…Además pueden ser la manifestación de un trastorno genético como la (9,10) esclerosis tuberosa . La Ecocardiografía convencional (Modo M, Bidimensional, Doppler Pulsátil, Continuo y Color), cuenta con nuevos e importantes avances de precisión morfológica en reconstrucciones Tri-Tetradimensionales, nuevas formas de evaluaciones funcionales como ecocardiografía con contraste, speckle tracking, strain rate, Doppler Tisular, etc., la han convertido en el método de elección en el diagnostico ya que determina la localización, e x t e n s i ó n , r e p e r c u s i ó n h e m o d i n á m i c a y características del tumor, y permiten continuar el (11) seguimiento con o sin resección quirúrgica . Sin embargo, cuando se necesiten otros métodos de diagnóstico por imagen no invasivos, como la R e s o n a n c i a M a g n é t i c a C a r d i a c a ( R M C ) o Angiotomografia cardiaca (TCC) pueden ser de un valor complementario.…”

Section: Corazón Más Frecuentemente a Los Grandes Vasos D O N D E Aunclassified

Tumores cardíacos de resorte quirúrgico. Serie de Casos

Garay¹,

Álvarez²,

Melgarejo³

et al. 2019

Pediatr (Asunción).

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Introducción: Los tumores cardiacos son infrecuentes en la edad pediátrica, en su mayoría son primarios y benignos (90%), siendo los más frecuentes los Rabdomiomas, Fibromas y Mixomas. Las indicaciones quirúrgicas están relacionadas al efecto hemodinámico o mecánico, arritmias y/o disfunción ventricular que ocasionan, más que a su origen anatomopatológico de benignidad o tamaño tumoral. En los tumores malignos o metastásicos la conducta a seguir la determina el origen primario del tumor, así como el estadio en que se encuentra cada paciente. Objetivos: Presentar la casuística y conducta médica de pacientes con Tumor Cardiaco sometidos a exéresis quirúrgica, así como su evolución inmediata y a mediano plazo. Material y Métodos: Análisis retrospectivo, observacional, mediante la revisión de datos de historias clínicas de niños diagnosticados con tumores cardiacos por ecocardiografía transtorácica. Resultados: En nuestra casuística, 4 de los 5 tumores fueron benignos (80%) y 1 maligno (20%); hubo 100% de coincidencia del hallazgo por Ecocardiografía bidimensional transtorácico de imagen de masa tumoral con el hallazgo quirúrgico; el diagnóstico histopatológico informó Mixoma en 3 casos (60%), 1 paciente (20%) Rabdomioma gigante y 1 paciente (20%) Carcionoma Mucoepidermoide de Timo. Encontramos correlación positiva entre el diagnóstico clínico-imageneológico y los resultados histopatológicos. Discusión: Los tumores cardiacos primarios benignos, tuvieron indicación de exéresis quirúrgica basados en su localización y repercusión hemodinámica obstructiva a las vías de entrada ventriculares. En el caso del carcinoma mucoepidermoide de timo de bajo grado de malignidad, el diagnóstico y resección quirúrgica precoz permitió la exéresis total, no requiriendo terapia adicional. La evolución posoperatoria sin complicaciones a excepción de un caso (20%) que requirió asistencia con ECMO. Todos fueron dados de alta y permanecen asintomáticos y sin regresión tumoral a 5 años del primer caso y 18 del ultimo. La ecocardiografía transtorácica bidimensional continúa siendo un método diagnóstico de elección para estos casos.

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Tumores cardíacos primarios en la infancia

Cited by 13 publications

References 14 publications

Neonatal supraventricular extrasystole as early clinical debut of cardiac rhabdomyoma

Neonatal supraventricular extrasystole as early clinical debut of cardiac rhabdomyoma

Primary Cardiac Tumors in Infancy: A Case Report and Literature Review

Tumores cardíacos de resorte quirúrgico. Serie de Casos

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