Tufted Angiomas: Variability of the Clinical Morphology

Abstract

In 1989 Wilson Jones and Orkin first described tufted angioma, which has the unifying histologic feature of circumscribed angiomatous tufts and lobules within the dermis. Tufted angioma may take unusual forms clinically. We describe five children less than 3 years of age with tufted angiomas, demonstrating the variability of the morphology of this vascular tumor. Two of the lesions were congenital. Three presented as indurated, vascular-appearing plaques, one of which had associated hypertrichosis. One lesion appeared clinically compatible with a hemangioma of infancy, but continued to enlarge after the child was 32 months old. The remaining lesion was a nearly circumferential, soft tissue tumor of the left forearm with tortuous vessels and a smaller overlying vascular stain. All of these lesions demonstrated the characteristic histology of tufted angioma. The clinical and histopathologic differential diagnosis as well as treatment options for tufted angioma are reviewed.

Congenital, Self-regressing Tufted Angioma

“…Ten reports of congenital or early-onset TA, all confirmed by histologic results, have been previously published in the literature [3][4][5][6][7] ; 4 of the lesions were congenital, 5 developed within the first 3 months of life, and 1 was noted by age 9 months. Tenderness or pain was noted in all.…”

Acquired tufted angioma: Case report

“…Tufted angioma can have variable presentations of mimicking pyogenic granuloma, hemangioma, vascular malformation or Kaposiform hemangioendothelioma (KHE) [8,9]. Our case was on the upper back in the presentation and it was a very welldefined papular lesion without any signs of vascular pathogenesis like a port wine stain, telangiectasia or any deeper tissue swelling.…”

Angioma em tufo e síndrome dolorosa miofascial

“…2,3 As the years went by, the lesion increased in size; however, it stabilized at puberty. Nevertheless, the pain intensified, making it difficult to move the affected limb, 8 which was already slightly hypotrophic.…”

“…It grows slowly and may present with overlying hypertrichosis and hyperhidrosis. 3 Although benign, the area affected is often extensive, resulting in a disfiguring appearance and impaired function if the condition is painful. Growth is slow and progressive, stabilizing in the majority of cases, and spontaneous involution may even occur.…”