“…The hallmark feature of SRD is the presence of ureteral duplication (duplex kidney), which is usually seen in neonates or children, and only rarely diagnosed in adulthood. [5][6][7] In approximately 25 reported adult cases with segmental dysplasia, patients had vesicoureteral reflux, ectopic ureter(s) with duplex and triplex kidney, ureteropelvic obstruction, hydroureter, voiding dysfunction, repeat urinary tract infections, abdominal pain, and genital anomalies. 5,7,8 Morphologically SRD is characterized by distorted cysts of various sizes lined by flattened to cuboidal epithelium, immature collecting ducts surrounded by fibromuscular collars and undifferentiated mesenchyme, blastema, islands of cartilage, and abortive glomerular structures.…”