Rhabdomyosarcome embryonnaire paratesticulaire : à propos d’un cas et revue de la littérature

Ghorbal, Lilia; Abid, Walid; Elloumi, F.; Sallemi, T.; Frikha, M.; Daoud, J.

doi:10.1016/j.canrad.2015.05.002

Cited by 4 publications

(11 citation statements)

References 14 publications

(33 reference statements)

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“…Il s'agit du 2eme cas traité dans notre institution durant 10 ans (4) en dehors des essais cliniques de l'IRS (intergroupe rhabdomyosarcoma study (I II II VI et V) et la SIOP (international society of pediatriconcology), la majorité des publications traitent des cas isolés [ 4 ]. La découverte clinique du rhabdomyosarcome paratesticulaire est souvent fortuite objectivant une masse intrascrotale indolore [ 5 ]. Devant une bourse aiguë non traumatique, le diagnostic est parfois difficile du fait de la présentation souvent confondue avec une torsion testiculaire, une tumeur testiculaire [ 5 , 6 ].…”

Section: Discussionunclassified

“…La découverte clinique du rhabdomyosarcome paratesticulaire est souvent fortuite objectivant une masse intrascrotale indolore [ 5 ]. Devant une bourse aiguë non traumatique, le diagnostic est parfois difficile du fait de la présentation souvent confondue avec une torsion testiculaire, une tumeur testiculaire [ 5 , 6 ]. En relevant des situations particulières, cliniques ou thérapeutiques, ces publications soulignent la difficulté en pratique clinique d'évoquer un tel diagnostic.…”

Section: Discussionunclassified

“…Elle permet d'objectiver la masse intra scrotale, développée aux dépens des enveloppes testiculaires ou le cordon spermatique. Le testicule est le plus souvent intact [ 5 , 8 ].…”

Section: Discussionunclassified

“…L'atteinte ganglionnaire lombo-aortique est rapportée dans 26% à 43% des cas. Le poumon, le foie et l'os sont les sites métastatiques les plus fréquents [ 5 ]. De ce fait La scanographie thoraco-abdomino-pelvienne contribue à l'appréciation de l'extension à distance de la maladie.…”

Section: Discussionunclassified

“…De ce fait La scanographie thoraco-abdomino-pelvienne contribue à l'appréciation de l'extension à distance de la maladie. La Scintigraphie osseuse, l'IRM ou la TEP-scanographie au FDG (fluorodésoxyglucose) ne font pas parti du bilan de routine et sont réservées à des présentations particulières [ 5 , 9 ]. La localisation paratésticulaire est considérée de bon pronostic par rapport à d'autres localisations comme l'orbite ou la région paraméningée [ 5 , 10 ].…”

Section: Discussionunclassified

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Un traumatisme scrotal négligé révélant un rhabdomyosarcome embryonnaire para-testiculaire: à propos d’un cas

Ahsaini¹,

Mellouki²,

Ouattar³

et al. 2018

Pan Afr Med J

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Le rhabdomyosarcome paratesticulaire embryonnaire est une tumeur mésenchymateuse rare qui représente une urgence diagnostique et thérapeutique. Les formes localisées sont de pronostic favorable et un traitement multimodal fait appel à la chirurgie, à la polychimiothérapie et à la radiothérapie permettant d'aboutir à d'excellents taux de survie globale. Nous rapportons un cas colligé dans notre service de rhabdomyosarcome embryonnaire para testiculaire à cellules fusiforme, caractérisé par une confusion clinique, chez un jeune patient de 17ans, et à l'occasion du quel nous reprendrons l'ensemble des caractères spécifiques de cette pathologie.

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Section: Discussionunclassified

“…Elle permet d'objectiver la masse intra scrotale, développée aux dépens des enveloppes testiculaires ou le cordon spermatique. Le testicule est le plus souvent intact [ 5 , 8 ].…”

Section: Discussionunclassified

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Un traumatisme scrotal négligé révélant un rhabdomyosarcome embryonnaire para-testiculaire: à propos d’un cas

Ahsaini¹,

Mellouki²,

Ouattar³

et al. 2018

Pan Afr Med J

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Surgical resection of a massive residual retroperitoneal mass after chemotherapy for a paratesticular rhabdomyosarcoma: a case report

et al. 2022

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Introduction Paratesticular rhabdomyosarcoma is a rare and aggressive mesenchymal tumor, accounting for only 7% of all rhabdomyosarcomas. It is mainly encountered in children and adolescents. The standard treatment consists of radical orchidectomy with negative surgical margins. However, chemotherapy is recommended to control retroperitoneal micrometastasis. The place of surgery for progressive retroperitoneal lymph node metastases remains controversial. We present a case of paratesticular rhabdomyosarcoma with progressive retroperitoneal lymph node metastases treated with surgery. Case report We report a case of a 17-year-old North African male with no particular medical history who presented with a left scrotal mass that had been evolving for several months. Beta-human chorionic gonadotropin, alpha-fetoprotein, and lactate dehydrogenase were normal. Scrotal ultrasonography revealed the presence of a 6 cm heterogeneous hypoechogenic tissular mass with cystic areas adherent to the left scrotal wall, which was thickened in some places and vascularized by color Doppler. It exerted a mass effect on the homolateral testicle, which was of average volume. The thoracic–abdominal–pelvic computed tomography scan showed the presence of suspicious paraaortic lymph nodes. The most voluminous one measured 16 × 23 mm2. A left orchidectomy was performed. The final pathology report revealed an 8 cm paratesticular rhabdomyosarcoma of the embryonic type that displaced the testicle without invading it. Without going beyond it, it infiltrated the epididymis, the rete testis, and the albuginea. The surgical margin at the level of the spermatic cord was free. The patient had adjuvant chemotherapy (ifosfamide, vincristine, and dactinomycin). The patient had a challenging paraaortic lymph node dissection since the mass enlaced the left ureter and renal vessels. On histological examination, the paraaortic lymph nodes were metastatic. Conclusion Rhabdomyosarcoma is an aggressive malignancy with high metastatic potential. Therefore, only an accurate diagnosis and early treatment can ensure better survival. Surgery in expert hands seems to be a good option for progressive retroperitoneal nodes. However, further studies are needed to determine the place of surgery in this setting.

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Case Report: The Paratesticular Rhabdomyosarcoma in Children

Azizi¹,

Babakhouya²,

Rkain³

et al. 2021

JCT

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Rhabdomyosarcoma is a rare and aggressive mesenchymal tumor, whose paratesticular location is the most common genitourinary site. It is the prerogative of the child and the young adult. On physical examination, a painless scrotal tumefaction is observed. His diagnosis is essentially provided by testicular ultrasound. His therapeutic strategy is codified and based on the combination of chemotherapy and surgical excision or radiotherapy. The precocity of the management and the accuracy of the extension and radiology tests are important for the vital and functional prognosis. We report a case of paratesticular rhabdomysarcoma of alveolar type, diagnosed in front of a large left painless scrotal mass, which has been evolving for less than one month in a 7-year-old child. An inguinal orchiectomy was performed. A histological examination of the excised tissue revealed an epididymal RMS of the alveolar type. Our patient had 9 chemotherapy sessions with vincristine, actinomycin C and cyclophosphamide. Each chemotherapy session took place over four days, with a 21-day cycle. He was evaluated for 4 years and demonstrated good clinical improvement. The experience gained from the index case is crucial for the management of patients with intratesticular rhabdomyosarcoma who must always ensure that the radical inguinal orchiectomy with lymph node dissection is covered by chemotherapy and/or radiotherapy. This will potentially reduce the chances of tumor recurrence and/or metastasis, thus improving patient prognosis.

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Rhabdomyosarcome embryonnaire paratesticulaire : à propos d’un cas et revue de la littérature

Cited by 4 publications

References 14 publications

Un traumatisme scrotal négligé révélant un rhabdomyosarcome embryonnaire para-testiculaire: à propos d’un cas

Un traumatisme scrotal négligé révélant un rhabdomyosarcome embryonnaire para-testiculaire: à propos d’un cas

Surgical resection of a massive residual retroperitoneal mass after chemotherapy for a paratesticular rhabdomyosarcoma: a case report

Case Report: The Paratesticular Rhabdomyosarcoma in Children

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