Renal Angiosarcoma: A Rare Primary Genitourinary Malignancy

Renal primary angiosarcoma

“…Some authors [14] advocate for the use of adjuvant radiotherapy for local control, as in soft tissue sarcomas, whereas others consider that it does not increase survival [5,15] and therefore chemotherapy should be administered at least for palliation although responses are short and relapses are very common.…”

Early diagnosis and straight forward surgery of an asymptomatic primary angiosarcoma of the kidney led to long‐term survival

“…To our knowledge, the presented case is the first primary renal angiosarcoma incidentally diagnosed by US and color Doppler US in an asymptomatic patients. Symptoms such as hematuria, 2,3 flank pain, 5,7–9 or B‐sypmtoms 6 are associated with the disease in all known cases of primary renal angiosarcoma. Characteristic histopathological features of angiosarcoma are cytologically malignant endothelial cells forming vascular structures.…”

“…Because of complete resection (R0), early stage of disease and no evidence of benefit for adjuvant therapy in literature, we decided against further treatment 3,6 …”

Spontaneous Rupture of a Renal Angiosarcoma

“…Renal angiosarcomas seem to have a predilection to occur in older white male patients, but 1 case documented thus far occurred in a woman [1]. A few aetiologic factors, one of them was trauma, have been suggested in angiosarcomas [2]. We were unable to identify a specific common factor in our case.…”

“…A primary angiosarcoma of the kidney is rarely reported (fewer than 15 cases) in the literature [1,2]. Yet, to our knowledge, this is the first report on a spontaneous rupture of a renal angiosarcoma.…”