Progressive Nature of Pigmented Paravenous Retinochoroidal Atrophy

ERG and EOG in progressive paravenous retinochoroidal atrophy

“…Patients with analogous fundus changes were described by several other authors (HsinHsiang, 1948;Archer, Krill and Ernest, 1972;Chisholm and Dudgeon, 1973;Francois and De Roucke, 1974;Pearlman et al, 1975Pearlman et al, , 1978and Skalka 1979). Noble and Carr (1983) reported the longest follow-up study of 21 years.…”

Inflammatory pigmented paravenous retinochoroidal atrophy

“…Optical coherence tomography revealed large cystoid areas in macular cross-sections. In PPRA it is likely that the fundus lesions may be slowly progressive 4,8,13 and that the fundus resembles retinitis pigmentosa with time. In a few patients, the fundus condition may be progressive and may be detected at an older age.…”

“…[1][2][3][4][5][6][7][8][9] This is an asymptomatic disease usually detected during routine ophthalmic examination. The condition is generally bilateral and young adults are most commonly affected.…”

Pigmented paravenous retinochoroidal atrophy (Review)

“…Certain patients who complained of poor dark adaptation, poor night vision or a blind eye did not suffer from PPRCA but instead had retinitis pigmentosa (RP) or pseudo PPRCA, as aforementioned (4,19,20,26,30,37). Particular observations in PPRCA have also been reported, including a shadow in front of the eye, diminished peripheral vision, mild pain and photopsia, involuntary closure of the upper eyelid, headaches and observing halos around lights (4,15,39). However, whether these observations are associated with the disease entity remains unknown.…”

“…Visual field changes may be normal. Depending on the topography of pigmentation and atrophy, the visual field may be manifested as a ring scotoma (20), a geographic scotoma, a quadrant defect (6), paracentral scotomas (4,17,20,26), concentric constriction (3,17,22,26,30,31,39), an enlarged blind spot (11,35) or scattered scotomas (41) corresponding to the atrophic paravenous areas. Color vision is usually normal, although mild non-specific dyschromatopsia or an acquired color vision defect has been observed in specific cases (13,26,30,31).…”