Periodontal Management of Sturge-Weber Syndrome

Kalakonda, Butchibabu; Koppolu, Pradeep; Mishra, Ashank; Reddy, Krishnanjaneya; Muralikrishna, Tupili; Lakshmi, Vijaya; Challa, Radhika

doi:10.1155/2013/517145

Cited by 5 publications

(9 citation statements)

References 6 publications

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“…1,2,3 Table 1 highlights the extra and intraoral features reported on previously SWS cases as well as its dental management, thus highlighting the role of the dentist on its diagnosis and treatment. 1,2,[4][5][6][7][8][9][10][11][12][13][14][15][16][17] The Roach Scale is used as a classification of the SWS manifestations: 18 Type 1 presents with facial and leptomeningeal angiomas and glaucoma may occur; Type 2 involves facial angioma alone -no CNS alteration is observed -and may have glaucoma and finally, type III shows isolated leptomeningeal angiomas and usually glaucoma. Furthermore, when the CNS and facial angiomas are present, SWS is referred to as complete, whereas it is incomplete when only one of these areas is affected.…”

Section: Discussionmentioning

confidence: 99%

A Contribuição da Odontologia no Diagnóstico e Manejo da Síndrome de Sturge-Weber: Relato de dois Casos

Rodrigues

Nunes

Almeida

et al. 2020

Rev. Bras. Odontol.

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Objetivo: O objetivo deste estudo foi relatar dois casos de pacientes do sexo feminino com diagnóstico de síndrome de Sturge-Weber (SSW), suas principais manifestações clínicas orais e maxilofaciais e tratamento odontológico. Relato de caso: Caso 1. Paciente do sexo feminino, 30 anos, encaminhada à Clínica de Estomatologia da Universidade Estadual do Rio de Janeiro para avaliação de lesão avermelhada difusa no rosto e na boca. Durante o exame clínico, foram detectadas manchas de vinho do porto (MVP) no lado direito da face e descoloração intraoral sugestiva de SSW. Como a paciente não referia sintomas, foi encaminhada a uma equipe de neurologia para investigar alterações no sistema nervoso central (SNC). Caso 2. Uma mulher de 19 anos foi encaminhada para avaliação de um sangramento gengival com duração de 5 meses na mucosa alveolar mandibular e maxilar direita. O exame extraoral mostrou a presença de MVP no lado direito do rosto. Ao exame intraoral, a hiperplasia gengival causou má oclusão, deposição de placa e sangramento grave. O diagnóstico de SSW foi estabelecido devido a esses achados. A paciente foi encaminhada para tratamento periodontal. Conclusão: Dessa forma, é essencial que o dentista tenha conhecimento das manifestações clínicas dessa síndrome, a fim de realizar seu diagnóstico e propor o tratamento correto

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Section: Discussionmentioning

confidence: 99%

A Contribuição da Odontologia no Diagnóstico e Manejo da Síndrome de Sturge-Weber: Relato de dois Casos

Rodrigues

Nunes

Almeida

et al. 2020

Rev. Bras. Odontol.

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“…The lesion extension over the midline is observed in 50% of the patients and bilateral involvement in 33% of the cases. 8 …”

Section: Discussionmentioning

confidence: 99%

Hypothyroidism and Sturge-Weber Syndrome associated with Bilateral Port-wine Nevus

Saroj

Gangwar

Dhillon

2016

International Journal of Clinical Pediatric Dentistry

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Sturge-Weber syndrome (SWS) is a rare, nonhereditary developmental condition that is characterized by a hamartomatous vascular proliferation of the brain, resulting in multiple angiomas that occur on the same side due to arteriovenous malformations. It is believed to be caused by persistence of a vascular plexus around the cephalic portion of the neural tube and is present at birth in about 1 in every 50,000 babies.It is one of the phakomatoses which is often associated with port-wine stains (PWSs) of the face, glaucoma, seizures, mental retardation and ipsilateral leptomeningeal angioma. Many people with SWS probably never know they have it. Hypothyroidism is a condition that arises from inadequate release of thyroid-stimulating hormone to stimulate an otherwise normal thyroid gland. This condition is often associated with a deficient secretion of other pituitary hormone, and growth hormone deficiency occurs with an increased prevalence in SWS, presumably secondary to involvement of the hypothalamic-pituitary axis. Diagnosis is made by the presence of a facial PWS and evidence of leptomeningeal angioma either by skull X-ray or computed tomography scan that shows intracranial calcifications. Presently, there is no specific treatment for SWS, and the management of the clinical manifestations and complications is still far from adequate.Here, we report the case of hypothyroidism associated with SWS with oral and facial manifestations in an 11-year-old boy.How to cite this article: Saroj G, Gangwar A, Dhillon JK. Hypothyroidism and Sturge-Weber Syndrome associated with Bilateral Port-wine Nevus. Int J Clin Pediatr Dent 2016;9(1): 82-85.

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“…Bu sendrom porto şarabı renkli nevus, leptomeningeal anjiom ve glokom gibi karakteristik bulgularının yanı sıra epilepsi, hemianopsi, hemiparazi, mental retardasyon gibi birçok bulguyu içeren, çok geniş klinik bulgular gösteren bir sendromdur. 11 Bu sendromun kliniksel olarak şiddeti Roach ölçeğine göre sınıflandırılmaktadır 14 ve sunduğumuz vaka Roach ölçeğine göre Tip 1 olarak sınıflandırılmıştır.…”

Section: Discussionunclassified

“…Bu durum oral bölgenin enfeksiyonlarına sebep olabilir ve kişinin sistemik sağlığını da etkileyebilir. 2,11 Sunduğumuz vakada hastamız mental reterdasyona, kollarda ve ellerde atrofiye sahipti. Mental retardasyon, fiziksel problemler ve antiepileptik ilaç kullanımı bu hastada oral hijyenin ciddi bir şekilde bozulmasına neden olmuştur.…”

Section: Discussionunclassified

“…6,7 Bu sendromda ana oküler bulgular sekonder olarak intraoküler tansiyonun artması ve koroidal hemanjioma bağlı olarak aköz humor sekresyonunun artmasından dolayı meydana gelen buftalmi ve glokomdur. [8][9][10][11] Klinik olarak fasial nevus, epilepsi, hemiparazi, hemiplaji, intrakranial kalsifikasyon ve mental retardasyon gibi önemli bulguları olan bu sendromun [12][13][14][15][16] kliniksel olarak şiddeti Roach ölçeğine göre yapılmaktadır. 14 Ölçekte sınıflandırma aşağıdaki şekilde yapılmaktadır:…”

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Sturge-Weber Sendromu:bi̇r Olgu Sunumu

Bayrakdar¹,

Çağlayan²,

Bilge³

2015

Atatürk Üniversitesi Diş Hekimliği Fakültesi Dergisi

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Sturge-Weber Syndrome is rare, nonhereditary, congenital neurocutaneous disease. Leptomeningeal hemanjiom, generally unilateral port wine nevus distributing trigeminal nerve region, ocular abnormally (glaucoma) are some parts of this syndrome. The present paper reports oral findings of a 18 years old female patient with Sturge-Weber Syndrome. Sturge-Weber Syndrome must be taken into account by dentists because of its various oral manifestations.

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Periodontal Management of Sturge-Weber Syndrome

Cited by 5 publications

References 6 publications

A Contribuição da Odontologia no Diagnóstico e Manejo da Síndrome de Sturge-Weber: Relato de dois Casos

A Contribuição da Odontologia no Diagnóstico e Manejo da Síndrome de Sturge-Weber: Relato de dois Casos

Hypothyroidism and Sturge-Weber Syndrome associated with Bilateral Port-wine Nevus

Sturge-Weber Sendromu:bi̇r Olgu Sunumu

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