Turner's syndromeis a condition involving total or partial absence of one X chromosomeand has been associated with a number of diseases including non insulin dependent diabetes mellitus, abnormalities of glucose metabolism and hypothreosis. There have been manycase reports in which Turner's syndrome is associated with type 2 diabetes, but the association with type 1 diabetes and/or life threatening complications is very rare. Wepresent an unusual case of a patient with Turner's syndrome whohas type 1 diabetes and is complicated with ketoaddosis, severe acute and recurrent pulmonary edema and rhabdomyolysis. (Internal Medicine 40: 418-420, 2001)