1961
DOI: 10.1001/archinte.1961.03620110121016
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Marfan's Syndrome and Dissecting Aneurysm of Aorta

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1963
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Cited by 12 publications
(4 citation statements)
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“…Skeletal manifestations include tall stature, long limbs and phalanges (arachnodactyly). Cardiovascular complications, particularly aneurysmal dilatation of the ascending aorta and dissections, are a major cause of death in the adult (Atta and Hoch, 1961 ;McKusick, 1955). The aortic lesion is thought to result from elastic fibre degeneration in the tunica media, producing cystic foci commonly termed medionecrosis (Erdheim, 1930).…”
Section: Introductionmentioning
confidence: 99%
“…Skeletal manifestations include tall stature, long limbs and phalanges (arachnodactyly). Cardiovascular complications, particularly aneurysmal dilatation of the ascending aorta and dissections, are a major cause of death in the adult (Atta and Hoch, 1961 ;McKusick, 1955). The aortic lesion is thought to result from elastic fibre degeneration in the tunica media, producing cystic foci commonly termed medionecrosis (Erdheim, 1930).…”
Section: Introductionmentioning
confidence: 99%
“…Case 1. Female, age 15, with clinical findings of arachnodactyly, pigeon breast, ectopia lentis, aortic regurgitation and great stature (175 cm) and with autopsy findings of diffuse and dissecting aneurysm in the ascending aorta and marked hypertrophy and dilatation of the left ventricle (550 gm).…”
Section: Methodsmentioning
confidence: 99%
“…Marfan's syndrome as (1) conglomerate, disorganized masses of hyperplastic and hypertrophied smooth muscle cell fibers, and (3) formation of greatly dilated vascular channels. One way or the other, a series of these regressive changes are the cause of dissecting or diffuse aneurysm frequently seen in Marfan's syndrome.…”
Section: Introductionmentioning
confidence: 99%
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