Intraatrial Conduit Repair in Scimitar Syndrome

Tsuchida, Koki; Anzai, N; Hashimoto, A; Fukushima, Yasunori; Yamada, Manabu

doi:10.1378/chest.92.6.1120

Cited by 9 publications

(5 citation statements)

References 4 publications

Supporting

Mentioning

Contrasting

Order By: Relevance

“…Puig-Massana and Revuelta [34] described use of the free wall of the right atrium to create a tunnel from the scimitar vein to the left atrium across an ASD. There have been two case reports utilizing a 14-mm Dacron graft [44] and a 20-mm Dacron graft [2] interposed between the orifice of the anomalous pulmonary vein and an enlarged ASD as an intra-atrial conduit [35].…”

Section: Treatment Modalities and Prognosismentioning

confidence: 99%

Eponym

et al. 2010

View full text Add to dashboard Cite

Scimitar syndrome is a rare congenital anomaly, characterized by partial or complete anomalous pulmonary venous drainage of the right or left lung into the inferior vena cava. The syndrome is commonly associated with hypoplasia of the right lung, pulmonary sequestration, persisting left superior vena cava, and dextroposition of the heart. The pathogenesis of the syndrome is unclear, but it seems to originate from a basic developmental disorder of the entire lung bud early in embryogenesis. Two main forms of scimitar syndrome have been described. Signs and symptoms can start during infancy (infantile form) or beyond (childhood/adult form). The infantile form generally presents within the first 2 months of life with tachypnea, recurrent pneumonia, failure to thrive, and signs of heart failure. The diagnosis of scimitar syndrome is usually made based on the characteristic chest X-ray films and can be confirmed by angiography; however, it is now done mostly by transthoracic or transesophageal echocardiography, noninvasive computed tomography, or magnetic resonance angiography. Fetal echocardiography using three-dimensional power Doppler imaging permits prenatal diagnosis. Most frequently, patients are asymptomatic in the absence of associated abnormalities and can be followed conservatively. For patients with congestive heart failure, repeated pneumonia, or pulmonary-to-systemic blood flow ratios greater than 1.5 and pulmonary hypertension, it is important to reroute the anomalous right pulmonary veins and repair the associated cardiac defects in order to avoid progression to right ventricular failure. The triad of respiratory distress, right lung hypoplasia, and dextroposition of the heart should alert the clinician to think of scimitar syndrome.

show abstract

Section: Treatment Modalities and Prognosismentioning

confidence: 99%

Eponym

et al. 2010

View full text Add to dashboard Cite

show abstract

“…Puig-Massana and Revuelta9 described use of the free wall of the right atrium to create a tunnel from the scimitar vein to the left atrium across an ASD. There have been two case reports utilizing a 14-mm Dacron graft10 and a 20-mm Dacron graft11 interposed between the orifice of the anomalous pulmonary vein and an enlarged ASD as an intra-atrial conduit.…”

Section: Discussionmentioning

confidence: 99%

Scimitar syndrome: report of a case and its surgical management

Rajaii-Khorasani

Kahrom

Mottaghi

et al. 2009

Annals of Saudi Medicine

View full text Add to dashboard Cite

“…4, the vein was deviated through the atrial septum into the left atrium, a technique which has been described in several other cases. In some of these cases, if the length of the scimitar was limited a patch sutured around an opening in the atrial septum or an interposition graft was used to make the connection with the left atrium [3,5,14,19,23,26,27]. In patient No.…”

Section: Discussionmentioning

confidence: 99%