Familial nevus sebaceus

Intraoral lesions associated with sebaceous nevus syndrome

“…The first reported the first case in this study. The second described a 3‐year‐old boy who had a sebaceous nevus that ‘extended around the angle of the mouth and onto the buccal mucosa as moist pink plaques’ 14 . Photographic documentation and histopathological data were not presented.…”

“…The second described a 3-year-old boy who had a sebaceous nevus that 'extended around the angle of the mouth and onto the buccal mucosa as moist pink plaques'. 14 data were not presented. Ectopic sebaceous glands on the intraoral mucosa have been previously reported, but not in association with cutaneous sebaceous nevi or the sebaceous nevus syndrome.…”

“…Sebaceous nevi usually occur sporadically, a feature that led to a belief that the sebaceus nevus is not a hereditary trait 12 . Although uncommon, reports of familial aggregation of sebaceus nevi are accumulating and run counter to this view 13–16 . It has been proposed that the sebaceus nevus may be inherited as a paradominant trait 17 .…”

“…12 Although uncommon, reports of familial aggregation of sebaceus nevi are accumulating and run counter to this view. [13][14][15][16] It has been proposed that the sebaceus nevus may be inherited as a paradominant trait. 17 Paradominant transmission explains the apparent non-Mendelian inheritance of autosomal mosaics.…”