Ectopic Secreting Choroid Plexus in the Oropharynx

Abstract

The authors report a case of an ectopic secreting choroid plexus in the oropharyngeal region of a neonate. The lesion presented as a rapidly growing tumor, containing CSF. No communication with the cranial cavity could be found. Following two surgical interventions the lesion was entirely removed and pathological examination revealed choroid plexus.

Case series of congenital heterotopic neuroglial tissue in the parapharyngeal space

“…Fewer than 20 cases of heterotopic neuroglial tissue in the parapharyngeal space have been reported in the literature [9][10][11][12][13][14] ( Table 1). The typical presentation in these cases is a neonate with clinical symptoms of airway obstruction or difficulty feeding with or without an accompanying palpable neck mass.…”

“…Airway obstruction is the foremost concern; however, even in young patients who are asymptomatic, resection may prevent future loss of cranial nerve function as the lesion enlarges. Management by drainage of these lesions has been shown to be complicated by rapid reaccumulation of fluid [12,20]. Recurrence in the event of incomplete excision has also been described [21].…”

Primary Choroid Plexus Papilloma of the Cauda Equina. A Case Report

“…The notion of ectopic choroid plexus has been described to explain the presence of choroid plexus tumors with no connection to the ventricular system 14,15 . Choroid plexus tissue has been described in cysts of the CPA, oropharynx and supratentorial cerebrum [18][19][20] . The other hypothesis set forth by Kurtkaya-Yapicier et al was that of choroid plexus metaplasia of ependymal cells 15 .…”

Ectopic presacral choroid plexus cyst in a neonate

“…Ectopic, secreting choroid plexus tissue had been described in occasional cystic lesions without ventricular communication. These include arachnoid cyst of the cerebellopontine angle [1], intracerebral supratentorial cyst [5], and oropharyngeal cyst of a neonate [4]. The embryologic basis of this ectopic tissue is thought to have arisen either from anomalous migration of choroid plexus tissue or by metaplasia from ependymal rests [3].…”