Ectodermal Dysplasia Treated With One-Step Surgical Rehabilitation: A Case Report

Abstract

Ectodermal dysplasia (ED) comprises a large heterogeneous group of inherited disorders that are characterized by primary defects in the skin, hair, nails, eccrine glands and teeth. The most characteristic findings are the reduced number of teeth. All rehabilitative programmes involve proper evaluation of skeletal relationships. Prosthetic-implantological treatment at the end of bony growth can be used. In this article a case of ED treated with Le Fort I for maxillary advancement, femur homografts, implants' insertion and immediate loading is described. In December 2007, a 38-year-old female was referred to the Maxillofacial Department of Galeazzi Hospital (Milan, Italy) who had a diagnosis of ED. Twelve implants were inserted in one-step surgical procedure. No implant was lost and all are stable. The occlusion is stable after 15 months of follow-up. The results indicate that the one-step oral rehabilitation can be performed in adults who are affected by ED. Also, this significantly reduces the time of oral and facial rehabilitation.

Systematic analysis on the efficacy of bone enhancement methods used for success in dental implants

“…Out of 31 included articles, 14 studies were using block graft. [ 32 33 34 35 36 37 38 39 40 41 42 43 44 45 ] Of which, 11 studies were case reports while three were prospective. A total of 86 patients with reduced alveolar ridges were treated with block grafts.…”

Complications of Implant Rehabilitation in Ectodermal Dysplasia Patients: A Review Study

“…(8) Typical appearance characteristics of HED patients comprise sparse hair, wide and prominent forehead and chin, saddle nose, dry skin, skin pigmentation around the eyes and the mouth, vision and hearing problems, periorbital wrinkles, lip thickening, mandibular protrusion, and dished-in midface. (3,5,9,10) Moreover, HED patients suffer from sensitivity to heat and frequent high fevers due to the absence or the significant decrease of sweat glands. (5,10,11) It is worth mentioning that sweat glands are normal in Hidrotic ED patients.…”

“…(3,5,9,10) Moreover, HED patients suffer from sensitivity to heat and frequent high fevers due to the absence or the significant decrease of sweat glands. (5,10,11) It is worth mentioning that sweat glands are normal in Hidrotic ED patients. (5) Oral findings include hypodontia or anodontia, delayed teeth eruption, root and crown dysmorphism, namely microdontia, anterior conical or peg-shaped teeth, posterior pyramidal and fused roots, and taurodontism, abnormal tooth germination, and dry mouth due to hypoplasia of the salivary glands.…”

“…(3,9) Moreover, dental implants should be placed only when the jaw relationship is corrected. (10) Therefore, in some cases, orthognathic surgery is necessary to correct the jaw relationship and skeletal deformity in order to achieve the best possible profile. (3) Insufficient bone support and poor retention due to xerostomia lead to patient discomfort with removable dentures.…”

Surgiplanner: A New Method for One Step Oral Rehabilitation of Severe Atrophic Maxilla

“…The implant-prosthetic rehabilitation of edentulous upper jaws has always been complex for surgeons and dentists (1)(2)(3)(4)(5)(6)(7)(8)(9)(10)(11)(12)(13). The lack of bone in both vertical and horizontal dimension does not allow the correct insertion of dental implants and oral rehabilitation (14)(15)(16)(17)(18)(19)(20)(21)(22).…”