Craniofacial fibrous dysplasia Report of a case with diverse radiological spectrum

Abstract

SummaryA young male of Asian-Indian ethnicity reported with a complaint of a painless, slow growing swelling over the left side of lower jaw. A thorough clinical history was taken and detailed radiological exam performed. The conventional radiographic examination revealed a mixed radiolucent-radiopaque lesion with unique appearances on different radiographs. Additional computed tomographic examination discovered the involvement of several bones in the skull base. Subsequent to histopathological confirmation a final diagnosis of craniofacial fibrous dysplasia was made. This case is particularly unique and of didactic importance as well because the various textbook descriptions for radiological appearances of fibrous dysplasia were found in the same case.

New technologies in oral radiology as a diagnostic aid for monostotic fibrous dysplasia: a review

“…Thus, cone beam computed tomography continues to be the most effective diagnostic method because of its utility in evaluating the lesion and establishing its relationship with adjacent structures. ( 9,25,27 ) According to the literature, different pathologies can be differentiated from monostotic fibrous dysplasia with the use of sequential or selective imaging methods. Nonetheless, the use of panoramic radiography combined with computed tomography provides greater information in relation to the description of the characteristics of this disease.…”

“…Thus, cone beam computed tomography continues to be the most effective diagnostic method because of its utility in evaluating the lesion and establishing its relationship with adjacent structures. 9 , 25 , 27 …”

“…These lesions are corroborated by biopsy examination, which can rule out other pathologies such as anosteogenic fibroma. 25 , 27 Advances in diagnostic methods have evolved from conventional radiographies for detecting monostotic fibrous dysplasia to digital radiographs which are easier to manage and improve the localization of the lesion in 2D images. These images show the lesions as radiopaque with non-precise limits, an absence of defined trabeculae, and demonstrate a possible relationship with adjacent bone structures.…”

Polyostotic Fibrous Dysplasia Differentiated in Intermediate-Grade Spindle Cell Sarcoma: A Case Report

“…Os sinais e sintomas podem variar dependendo da região afetada. Podem se apresentar desde um estado assintomático de deformidade facial até consequências mais graves, como alterações na visão, deficiência auditiva e obstrução nasal (Lee et al, 2012;Punyani, Srivastava, & Jasuja, 2016).…”

“…Cerca de 10 a 27% dos casos da forma monostótica têm envolvimento de ossos cranianos. Na forma poliostótica o número chega a 50% dos casos, com comprometimento de ossos etmoidais, esfenóides, frontais, maxilares, temporais e occipitais em ordem decrescente de frequência (Punyani, Srivastava, & Jasuja, 2016;Sandhu, Sandhu, & Sabharwal, 2012).…”