Congenital conductive hearing loss

Raveh, Eyal; Wei-li, HU; Papsin, Blake C.; Forte, Vito

doi:10.1258/0022215021910014

Cited by 52 publications

(48 citation statements)

References 14 publications

(19 reference statements)

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“…The stapes footplate fixation malformation (class I according to the Teunissen and Cremers classification) is thought to be the most common isolated middle ear anomaly and has been the subject of serial analyses more frequently than any other category of anomalies [Teunissen et al, 1990;Hashimoto et al, 2002;Raveh et al, 2002;Hung et al, 2003;. Similar to the observations of Kojima et al , ossicular malformations associated with a mobile footplate were predominant (57.6%) in our study, while stapes fixation was found in 24.2% of cases and stapes fixation with other ossicular malformations in 18.2% of cases.…”

Section: Discussionmentioning

confidence: 99%

Congenital Middle Ear Anomalies: Anatomical and Functional Results of Surgery

Quesnel

Benchaa²,

Bernard³

et al. 2015

Audiol Neurotol

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The aim of this study was to describe the audiometric results following surgery in a consecutive series of pediatric patients with a congenital middle ear disorder. Retrospective chart review was performed for 29 consecutive children who underwent 33 middle ear surgeries for congenital ossicular chain anomaly between 1990 and 2012. Anomalies were classified into four groups according to the Teunissen and Cremers classification. Audiological parameters using four frequency averages (0.5, 1, 2 and 4 kHz) were assessed pre- and postoperatively. Clinical and audiometric follow-up times were, respectively, 49 ± 8 and 35 ± 5 months (mean ± SEM). Fifty-eight percent of all patients achieved an air-bone gap (ABG) ≤20 dB, 62.5% in class I, 50% in class II and 57.9% in class III. The improvement of the mean ABG was 13.6 dB, 19.2 dB for class I, 0.2 dB in class II and 15.4 dB in class III. Overall mean pure-tone averages improved 14.8 dB with 13.9 dB for class I; there was no improvement for class II and 20.2 dB for class III. The sensorineural hearing loss rate was 9%. This pediatric series showed that hearing results depend on type of anomaly. Class I and class III showed better hearing improvement than class II.

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Section: Discussionmentioning

confidence: 99%

Congenital Middle Ear Anomalies: Anatomical and Functional Results of Surgery

Quesnel

Benchaa²,

Bernard³

et al. 2015

Audiol Neurotol

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“…Nevertheless, they are clinically important because hearing loss can be corrected by an appropriate procedure. The most common congenital isolated ossicular anomalies are stapes fixation and incudostapedial discontinuity [14]. Several authors report the prevalence of isolated congenital stapes fixation between 20 and 35 % of ossicular malformations [15,16].…”

Section: Discussionmentioning

confidence: 99%

Stapes malformations: the contribute of the endoscopy for diagnosis and surgery

Marchioni

Soloperto

Villari

et al. 2015

Eur Arch Otorhinolaryngol

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The aim of this study is to investigate the contribute of the endoscopic exclusive transcanalar approach for the management of stapes malformations. A retrospective chart review was made at our tertiary referral centers. 17 patients with stapes malformations underwent surgery with endoscopic exclusive transcanal approach. A complete audiological and radiological assessment before and after surgery was performed. 12/17 (70 %) underwent a surgical endoscopic correction, In case of fixed platina underwent five endoscopic stapedotomy and one endoscopic stapedectomy were performed. In case of mobile platina five endoscopic ossiculoplasties with partial ossiculoplasty replacement prosthesis were performed, 3 with autologous remodeling incus and 2 with malleus head remodeling. In 1 case, only an endoscopic stapes mobilization was made. In 5/17 (30 %), due to difficult anatomical findings an endoscopic explorative tympanotomy was finally performed. The mean preoperative air conduction (AC), bone conduction (BC) and air-bone gap (ABG) were, respectively, 60.7, 26.3 and 34.4 dB. The mean postoperative AC, BC and ABG were, respectively, 33.8, 26.5 and 7.3 dB, with a mean improvement of the ABG of 27.1 dB. Discharge from hospital was on the first post-surgery day. No relevant postoperative complications were noted. The median follow-up was 3.6 years (range 1-6). The endoscopic approach results very adequate for the diagnosis and treatment of stapes malformations, checking variations of the ossicles conformation and functioning and performing safe surgery, under direct control of middle ear structures.

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“…Jahrsdoerfer [3] reported a large series of 50 operated cases of minor congenital malformations of the ear, but none of these had similar abnormalities to the present case. Raveh et al [4] reviewed the charts of 416 children who underwent tympanotomy between 1986 and 1996 in the Hospital for Sick Children in Toronto, a large tertiary referral center. Sixty-seven of these were operated for congenital conductive hearing loss of unknown origin.…”

Section: Discussionmentioning

confidence: 99%

Late Detection of Hearing Loss in a Case with Middle Ear Congenital Abnormality

Tzangaroulakis¹,

Korres²,

Alatzidou³

et al. 2002

Otorhinolaryngol Nova

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The present paper describes a rare case of a unilateral congenital ossicular abnormality that presented in adulthood. A unilateral conductive hearing loss was revealed during a routine examination for a professional driving license. Differential diagnosis included otosclerosis and ossicular anomalies. Our patient, a 40-year-old man, had no history of otitis media or trauma to the head and he was not aware of his hearing loss. Exploratory tympanotomy revealed absence of the long process of the incus and of the stapes. A remnant of the underdeveloped stapes footplate was removed and reconstruction of the defect using a 5.0-mm malleus-oval window prosthesis had an excellent result with complete restoration of the air-bone gap. The patient experienced binaural hearing with great excitement.

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Congenital conductive hearing loss

Cited by 52 publications

References 14 publications

Congenital Middle Ear Anomalies: Anatomical and Functional Results of Surgery

Congenital Middle Ear Anomalies: Anatomical and Functional Results of Surgery

Stapes malformations: the contribute of the endoscopy for diagnosis and surgery

Late Detection of Hearing Loss in a Case with Middle Ear Congenital Abnormality

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