Classical oral manifestations of Dyke-Davidoff-Masson syndrome: a case report with review of the literature

Kalaskar, Ritesh; Kalaskar, Ashita

doi:10.5125/jkaoms.2018.44.4.198

Cited by 9 publications

(5 citation statements)

References 21 publications

(32 reference statements)

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“…While the symptoms of the infantile variety first appear during pregnancy or infancy, those of the acquired kind first show up throughout puberty or adulthood [8]. In a few cases, there may be ipsilateral Café au lait pigmentations and ocular lipodermoid, contralateral delayed teeth eruption, hypoplasia, and taurodontism [9]. The signs of DDMS may be so minor that conventional radiographs fail to pick them up.…”

Section: Discussionmentioning

confidence: 99%

Dyke-Davidoff-Masson Syndrome: A Classic Case Report

Dhawan¹,

Rathod²,

Dhok³

et al. 2023

Cureus

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Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological disorder found in children as well as adults. It is characterized by hemi cerebral atrophy. To date, very few cases of this disorder have been reported. Radiological imaging including magnetic resonance imaging (MRI) and computed tomography (CT) are accurate tools for the diagnosis of DDMS. We present a case of a 13-year-old female child who came with complaints of multiple episodes of generalized tonic-clonic seizures. In our case, clinical history and imaging with CT and MRI were accurate enough to diagnose DDMS.

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Section: Discussionmentioning

confidence: 99%

Dyke-Davidoff-Masson Syndrome: A Classic Case Report

Dhawan¹,

Rathod²,

Dhok³

et al. 2023

Cureus

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“…The congenital form states that the cerebral insult likely occurred in-utero due to vascular malformation, cerebral infarction, coarctation of the mid-aortic arch, gestational vascular occlusion, and infections. In the acquired form, the cerebral insult likely occurred during the perinatal or postnatal period, caused by hypoxia, birth trauma, tumors, infections, prolonged febrile seizures, and intracranial hemorrhage [8]. In both sexes, either of the hemispheres can be affected by DDMS.…”

Section: Discussionmentioning

confidence: 99%

Dyke-Davidoff-Masson Syndrome: A Case Report

Chunchu¹,

Kommalapati²,

Pemma³

et al. 2023

Cureus

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Dyke-Davidoff-Masson syndrome (DDMS) is a rare neurological entity that is predominantly seen in childhood. Here, we present the case of a 13-year-old girl who was brought to the pediatric ward for general examination with a previous history of seizures, speech difficulty, facial deviation, and progressive leftsided hemiparesis that started at the age of two, followed by delayed developmental milestones. Computed tomography (CT) and magnetic resonance imaging (MRI) of the brain showed right cerebral hemiatrophy, ventriculomegaly, hyperpneumatization of the sinus, the decreased caliber of cortical veins, and skull thickening on the right were all characteristic findings of DDMS. Based on the history, clinical presentation, and imaging findings from CT and MRI, DDMS was confirmed. Identifying DDMS in a clinical setting can be challenging because of low awareness of the condition and varied clinical presentations. Although CT and MRI imaging are the gold standards in diagnosing DDMS, the early manifestations of the disease cannot be well-appreciated on a CT and would likely require an MRI. Since there is no standardized protocol for managing DDMS, the treatment is primarily symptomatic. Early identification and diagnosis of the syndrome are essential to aid the child's mental and physical development through a multidisciplinary approach. There is also a need to improve awareness of DDMS so that the condition can be considered a potential differential diagnosis amongst other similar conditions and does not get misdiagnosed. The lack of a proper protocol for the management of DDMS prompts more research for a better understanding and early identification of the condition.

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“…In contrast, we report adult population in northern Tanzania to have brain atrophy which is not associated with paranasal infection. Although, the enlargement of the paranasal sinuses, mastoid cells and calvarial thickening have been reported in patients with cerebral hemi-atrophy [ 48 , 49 ]. As the pathogenesis of sinusitis to the central nervous system (CNS) has not been well explored globally.…”

Section: Discussionmentioning

confidence: 99%

Prevalence and risk factors of brain atrophy and associated confusion state among adults from three hospitals in northern Tanzania

Joseph¹,

Mpolya²,

Vianney³

2023

Pan Afr Med J

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Introduction brain atrophy is the reduction of brain volume often accompanied with cognitive changes. Despite the availability of computerized-tomography (CT) scanners in Tanzania, little is known about the magnitude of brain atrophy, its associated confusion state and the risk factors in adults. This study aimed to fill those knowledge gaps. Methods a retrospective cross-sectional hospital-based survey was conducted in northern Tanzania using a sample size of 384 CT images of adults who underwent brain CT scans in three referral hospitals. CT images were evaluated using a diagonal brain fraction (DBF) method to determine the presence of brain atrophy. Data for other covariates were also collected. Results we report a prevalence of 60.67% for brain atrophy and 35% for the associated confusion state. Association between confusion state and brain atrophy was statistically significant (χ 2 = 21.954, p<0.001). Brain atrophy was prognosticated by: age (adjusted OR: 1.11; 95% CI [1.05, 1.20], p<0.001), smoking (adjusted OR: 6.97; 95% CI [2.12, 26.19], p<0.001), alcohol-consumption (adjusted OR: 11.87; 95% CI [3.44, 40.81], p<0.001), hypertension (adjusted OR: 61.21; 95 CI [15.20, 349.43], p<0.001), type-2 diabetes mellitus (adjusted OR: 15.67; 95% CI [5.32, 52.77], p<0.001) and white matter demyelination (adjusted OR: 13.45; 95% CI [4.66, 44.25], p<0.001). Conclusion there is high prevalence of brain atrophy and associated confusion state among hospitalized adults in northern Tanzania. Reported prognostic factors for brain atrophy such as age, smoking, alcohol consumption, hypertension, type-2 diabetes mellitus and white matter demyelination could help focus interventions in this area.

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Classical oral manifestations of Dyke-Davidoff-Masson syndrome: a case report with review of the literature

Cited by 9 publications

References 21 publications

Dyke-Davidoff-Masson Syndrome: A Classic Case Report

Dyke-Davidoff-Masson Syndrome: A Classic Case Report

Dyke-Davidoff-Masson Syndrome: A Case Report

Prevalence and risk factors of brain atrophy and associated confusion state among adults from three hospitals in northern Tanzania

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