Bullous Congenital Ichthyosiform Hyperkeratoses

Nevus comedonicus with Epidermolytic Hyperkeratosis

“…In this case the EH oc curred not only in the follicular epithelium Table I. Occurrence of EH in other dermatoses Bullous ichthyosiform erythroderma [7,8] Nevus unius lateris [9,10] Ichthyosis hystrix [10] Keratoderma palmariset plantaris [11] Solitary epidermolytic acanthoma [12] Disseminated epidermolytic acanthoma [13,14] Epidermolytic leukoplakia [15,16] Acrosyringial epidermolytic papulosis neviformis [17] I ncidental finding in a variety acquired solitary skin le sions [18,19] but also in the sebaceous ducts, and was as sociated with dyskeratotic cells and corps ronds in some specimens. Barsky et al [4] reported this variety of nevus comedonicus in 4 patients, 1 of whom had been previously described by Montgomery [20].…”

Ichthyosis hystrix

“…Therefore, some authors [7][8][9] believe that IH is a clinical variant of BCIE and probably represents a different expression of a pleiotropic domi nant gene [10,11]. This hypothesis is strengthened by the occurrence of both dis eases in the same family [12].…”

Epidermolytic Hyperkeratosis Associated with a Dilated Pore

“…Although EH is a histologically descriptive diagnosis, it was first applied to a specifi~constellation of clinical disorders, including congenital bullous ichthyosiform erythroderma, linear epidermal nevus, and a certain form of palmoplantar keratoderma (2)(3)(4). Later, some acquired solitary lesions have also been reported to display EH as an incidental finding (1,5).…”