Bronchoscopic concerns in Proteus syndrome: a case report

Abstract

Proteus syndrome (PS) is a rare congenital hamartomatous disorder with multisystem involvement. PS shows highly clinical variability due to overgrowth of the affected areas, and several features can make anesthetic management challenging. Little is known about the airway problem associated with anesthesia in PS patients. An 11-year-old girl with PS was scheduled for ear surgery under general anesthesia. She had features complicating intubation including facial asymmetry and disproportion, abnormal teeth, limitation of neck movement due to torticollis, and thoracolumbar scoliosis. This study reports on a case of deformed airway of a PS patient under fiberoptic bronchoscopy.

Proteus syndrome in pregnancy: A case report

“…General anaesthesia in itself carries a higher risk to obstetric women compared with the general population, such as failed intubation, airway oedema and ventilation difficulties. 17 Additionally, women with Proteus syndrome may have obstructive or restrictive lung disease which further increases their risk during general anaesthesia. 18 Our patient did not have any obstruction or restrictive lung disease.…”