“…3 Due to its presentation at different ages and with different stages of pulmonary hypertension, it is important to determine the appropriate therapeutic approach, without a consensus on its management. Thereby, Batlivala et al 7 highlight the importance of an early diagnosis and intervention to optimize long-term results, recommending the initial diagnosis with cardiac catheterization or magnetic resonance imaging to adequately identify the anatomy and perform pulmonary unifocalization early, coinciding with Varghese et al 8 that recognition of the anatomy is essential since it proposes reconnection in patients with origin of RPA from the brachiocephalic trunk with a flap from the MPA. Krammoh et al 5 propose a two-stage strategy, with the placement of an intraductal stent followed by direct surgical reconnection or a prosthetic graft, coinciding with the series by Mery et al, 9 where they performed centralization, a surgical connection between the MPA and RPA, in a single stage in 2 patients.…”