Rehabilitation of pulmonary arteries: hybrid treatment in the unilateral absence of the pulmonary artery.

Cervantes-Salazar, Jorge; García-Montes, José Antonio; Peralta-Santos, Henry; Ortega-Zhindón, Diego B; Calderón‐Colmenero, Juan

doi:10.22541/au.161314215.58819168/v1

Cited by 2 publications

(2 citation statements)

References 5 publications

(7 reference statements)

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“…We could achieve this in two of our patients to date; with a third awaiting surgery. Comparable strategies have been described earlier [10] and are still applied [11]. In case of stenosis of the reimplanted vessel, percutaneous treatment can be performed.…”

Section: Discussionmentioning

confidence: 99%

“Absent” unilateral pulmonary arteries aren't absent, but disconnected. Review of the current literature based on 4 cases

Krasemann¹,

Dalinghaus²,

Beynum³

et al. 2022

Rev. Cardiovasc. Med.

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Background: Disconnected unilateral pulmonary arteries are frequently misdiagnosed as "absent". They typically arise from the base of the innominate artery and are fed by an aberrant arterial duct. If diagnosed early enough, they can be reconnected with catheter techniques even after closure of this aberrant duct. Consecutive surgical anatomical correction at a later stage is possible. Methods: Four cases illustrate the anatomical findings on computed tomography and angiography, all show an outpouching at the base of the brachiocephalic artery. Results: The therapeutic approach consisted of stenting of the aberrant ductus and consecutive surgery. In the oldest patient, 13 years, such an approach was impossible. Conclusion: If identified early in life, disconnected pulmonary arteries can be recruited with catheter techniques, and reconnected surgically at a later stage. It is not yet known if this approach prevents pulmonary damage, which is frequently seen in older untreated patients.

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Section: Discussionmentioning

confidence: 99%

“Absent” unilateral pulmonary arteries aren't absent, but disconnected. Review of the current literature based on 4 cases

Krasemann¹,

Dalinghaus²,

Beynum³

et al. 2022

Rev. Cardiovasc. Med.

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show abstract

“…7 Surgical treatment such as revascularization with aortopulmonary shunt creation, PA anastomosis, and novel hybrid techniques utilizing intraductal stents is indicated in childhood and feasible as PA branch rescue may result in normalization of pulmonary pressure and avoidance of lung transplant. 1,8 However, in older adult patients, surgical options with revascularization are not feasible because the intrapulmonary arteries are largely fibrosed. 1,7 Therefore, pharmacotherapy with vasodilators is largely pursued in patients with PH.…”

Section: Discussionmentioning

confidence: 99%

Pulmonary hypertension in an adult with unilateral absence of left pulmonary artery

Ghazarian

King

Premyodhin

et al. 2022

SAGE Open Medical Case Reports

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Unilateral absence of pulmonary artery is a rare congenital abnormality that occurs due to malformation of the sixth aortic arch during embryonic development. The clinical presentation of unilateral absence of pulmonary artery can vary based on age of diagnosis; however, in the adult population, it can present with a variety of manifestations including hemoptysis, recurrent pneumonia, and pulmonary hypertension or as an incidental finding. Diagnosis and management of unilateral absence of pulmonary artery remain a challenge. Here, we describe a case of a 37-year-old female with no known past medical history who presented with progressively worsening dyspnea and fatigue. She was incidentally found to have unilateral absence of pulmonary artery on computerized tomography angiography of the chest. Her imaging and physical exam demonstrated signs of volume overload and severe pulmonary hypertension. She received diuretics with good response and was discharged with referral to pulmonary hypertension clinic and eventual follow-up with right heart catheterization. In summary, we describe a rare congenital condition and highlight its diagnostic and therapeutic challenges.

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Rehabilitation of pulmonary arteries: hybrid treatment in the unilateral absence of the pulmonary artery.

Cited by 2 publications

References 5 publications

“Absent” unilateral pulmonary arteries aren't absent, but disconnected. Review of the current literature based on 4 cases

“Absent” unilateral pulmonary arteries aren't absent, but disconnected. Review of the current literature based on 4 cases

Pulmonary hypertension in an adult with unilateral absence of left pulmonary artery

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