Rehabilitation of pulmonary arteries: Hybrid treatment in the unilateral absence of the pulmonary artery

Abstract

Background Unilateral abscence of pulmonary artery is a rare congenital heart disease. If these anomaly is unrecognized and treated the risk of pulmonary hypertension in the contralateral lung can be lethal for the patients. Aims To report the successful sequential hybrid‐surgical approach of two cases of rescue of pulmonary branches only fed by ductus arteriosus. Materials & Methods Description of two rare cases of absence of a unilateral pulmonary branch successfully treated in our institution. Results, Discusssiion and Conclusion The timely identification of these cases and the strategic planning of interventional and surgical hybrid sequential treatment of these rare cases is effective.

Pulmonary hypertension in an adult with unilateral absence of left pulmonary artery

“… 7 Surgical treatment such as revascularization with aortopulmonary shunt creation, PA anastomosis, and novel hybrid techniques utilizing intraductal stents is indicated in childhood and feasible as PA branch rescue may result in normalization of pulmonary pressure and avoidance of lung transplant. 1 , 8 However, in older adult patients, surgical options with revascularization are not feasible because the intrapulmonary arteries are largely fibrosed. 1 , 7 Therefore, pharmacotherapy with vasodilators is largely pursued in patients with PH.…”