A case of glaucoma associated with Sturge-Weber syndrome and Nevus of Ota

Lee, H; Choi, SeongJu; Kim, S S; Hong, Young Jae

doi:10.3341/kjo.2001.15.1.48

Cited by 11 publications

(3 citation statements)

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“…2 ACG is a rare presentation in SWS, which has been reported as a consequence of ectopia lentis, posterior scleritis, chronic uveitis and alteration of the ciliary body configuration secondary to diffuse choroidal hemangioma. [5][6][7][8][9] However, unlike our case, all these case reports had a unilateral secondary angle closure mechanism associated with SWS. In the present case, the patient had ACG in the contralateral eye, too and all possibilities of a secondary angle closure mechanism were ruled out with the help of investigations.…”

Section: Discussioncontrasting

confidence: 57%

Sturge-Weber Syndrome Associated with Bilateral Angle-closure Glaucoma in a Young Adult

Dr PARAALI SHAH,

Dr Mithun Thulasidas,

Dr AJITA SASIDHARAN

2023

IJCP

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Sturge-Weber syndrome (SWS) is a phakomatosis involving the eyelids, conjunctiva, choroid and retina. The mechanism ofglaucoma in SWS involves developmental anomaly of the anterior chamber angle and elevated episcleral venous pressure.Here, we present a case of Roach’s type II SWS with bilateral angle-closure glaucoma (ACG) in a young adult, which to thebest of our knowledge, is the first-of-its-kind report in the literature. Though unusual, ACG may occur in young adults too.However, the underlying causes that make them develop the ACG are poorly understood. We also highlight the importanceof comprehensive clinical examination and appropriate investigations for early detection and proper treatment of such youngpatients with ACG.

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Section: Discussioncontrasting

confidence: 57%

Sturge-Weber Syndrome Associated with Bilateral Angle-closure Glaucoma in a Young Adult

Dr PARAALI SHAH,

Dr Mithun Thulasidas,

Dr AJITA SASIDHARAN

2023

IJCP

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“…The Nevus of Ota is a melanocytic pigmentary disorder, most commonly involving the area innervated by the trigeminal nerve. Elevated intraocular pressure, with or without glaucomatous damage, is observed in 10% of the cases (75). Episcleral venous telangiectasia vessels were prominent features.…”

Section: Renal Cyst and Ocular Abnormalitiesmentioning

confidence: 96%

Eye and Kidney

Izzedine¹,

Bodaghi

Launay-Vacher³

et al. 2003

Journal of the American Society of Nephrology

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“…All patients positively responded to treatment with anti-glaucoma drugs and topical steroids and surgery was not required [81]. The detection of progression of damage shown by visual field defects or SDOCT alterations of the optic nerve, together with the failure to reach target pressure indicates the need to evaluate filtering or valve surgery [80,82].…”

Section: Glaucoma Treatmentmentioning

confidence: 99%

An update on ophthalmological perspectives in oculodermal melanocytosis (Nevus of Ota)

Abdolrahimzadeh

Pugi

Manni

et al. 2022

Graefes Arch Clin Exp Ophthalmol

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Purpose To provide a review of the literature on oculodermal melanocytosis (ODM) with a focus on the diagnostic and therapeutic implications of multimodal imaging techniques in the management of ophthalmic complications. Methods The authors carried out a literature search on PubMed, Medline, and Scopus of English language articles published on ODM through August 2021. This review presents traditional and novel diagnostic methods in the diagnosis and follow-up of patients with particular emphasis on addressing the role of imaging in the management of the ophthalmic complications of the condition towards improving current practice patterns. Results ODM is a rare, prevalently unilateral, congenital condition that presents with brown or blue/gray flat asymptomatic lesions of the skin, mucosae, episclera/sclera, and uvea localized within the territory of distribution of the ophthalmic and mandibular branches of the trigeminal nerve. Glaucoma and predisposition to uveal melanoma are the main ophthalmic complications. Diagnosis and management are through comprehensive opthalmological examination and traditional imaging methods such as ultrasonography and fluorescein/indocyanine green angiography as pigmentation of the fundus can conceal subtle retinal and choroidal alterations. Anterior segment optical coherence tomography and ultrasound biomicroscopy are used to evaluate the anterior segment and the ciliary body in the presence of glaucoma or melanoma of the anterior uveal tract. Fundus autofluorescence and retinal pigment epithelium (RPE) alterations are of aid in the differential diagnosis between choroidal nevi and melanoma. Enhanced depth imaging spectral domain optical coherence tomography offers outstanding in vivo evaluation of the dimensions and details of tumors or nevi and surrounding choroidal tissues and small choroidal melanomas may show distortions of the retinal and sub-retinal profile, presence of intra and sub-retinal fluid, abnormalities of the RPE, and compression of the choriocapillaris. Conclusions Novel multimodal imaging techniques are significant in the diagnosis and management of the ophthalmic complications of ODM. Fundus autofluorescence and enhanced depth spectral domain optical coherence tomography have adjunctive value in the detection of early-stage melanoma and differential diagnosis between nevi and melanoma. Awareness of current and emerging imaging techniques can propagate improved standardized definition and assessment of the complications of ODM.

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A case of glaucoma associated with Sturge-Weber syndrome and Nevus of Ota

Cited by 11 publications

References 0 publications

Sturge-Weber Syndrome Associated with Bilateral Angle-closure Glaucoma in a Young Adult

Sturge-Weber Syndrome Associated with Bilateral Angle-closure Glaucoma in a Young Adult

Eye and Kidney

An update on ophthalmological perspectives in oculodermal melanocytosis (Nevus of Ota)

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