Sturge-Weber Syndrome Associated with Bilateral Angle-closure Glaucoma in a Young Adult

Abstract

Sturge-Weber syndrome (SWS) is a phakomatosis involving the eyelids, conjunctiva, choroid and retina. The mechanism ofglaucoma in SWS involves developmental anomaly of the anterior chamber angle and elevated episcleral venous pressure.Here, we present a case of Roach’s type II SWS with bilateral angle-closure glaucoma (ACG) in a young adult, which to thebest of our knowledge, is the first-of-its-kind report in the literature. Though unusual, ACG may occur in young adults too.However, the underlying causes that make them develop the ACG are poorly understood. We also highlight the importanceof comprehensive clinical examination and appropriate investigations for early detection and proper treatment of such youngpatients with ACG.