Pemphigus Vegetans Associated With Verrucous Lesions - Expanding a Phenotype

Multiple vegetating plaques on a Cesarean section scar

“…Our patient had painful erosions on her lips with crusts and fissures with a cobblestone pattern. According to de Almeida, the involvement of the vermilion border of the lips is a clinical hallmark of oral involvement. The tongue may also be involved with scrotal or cerebriform‐like changes .…”

Cobblestone mouth: An exuberant oral presentation of pemphigus vegetans

“…1,2 Involvement of the vermilion border of the lips is a clinical hallmark of oral involvement. 3 The tongue may show cerebriform-like changes. 1 The exuberant cobblestone pattern of the lips and oral mucosa associated with marked weight loss in the current case highlights the importance of oral manifestations of pemphigus vegetans.…”

Pemphigus vegetans with paronychia‐like changes resistant to rituximab therapy

“…1 Pemphigus vegetans (PVeg) is a rare clinical variant of PV, making up about 2% of all cases. 1 PVeg is distinguished from PV by the presence of vegetative plaques, most commonly on the oral mucosa or intertriginous areas. There are two clinical subtypes of PVeg: Hallopeau type and Neumann type.…”

“…There are two clinical subtypes of PVeg: Hallopeau type and Neumann type. 1 The Hallopeau type follows a milder disease course and does not usually have mucosal involvement. On the other hand, the Neumann type is more severe and is often characterized by associated mucosal involvement.…”