Agenesis or pseudoagenesis of the dorsal pancreas

Guimarães, Alberto Brunning; Guimarães, Carlos Alberto; Manso, José Eduardo Ferreira

doi:10.1590/0100-69912015005015

Cited by 11 publications

(8 citation statements)

References 8 publications

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“…These include the ectopic spleen, bowel malrotation, heterotaxy syndrome, left-sided gallbladder, choledochal cyst, pancreatic anomalies, and bile duct anomalies, and cardiac anomalies. [ 13 ] However, the association of genitourinary anomalies with dorsal agenesis of the pancreas has not been common and is also counterintuitive because the pancreas is of endodermal origin and genitourinary structures like kidney or uterus are of mesodermal origin. In 2015, Lal et al .…”

Section: Discussionmentioning

confidence: 99%

A case of dorsal agenesis of pancreas associated with unilateral renal agenesis, unicornuate uterus, and ovarian ectopia: A brief review and learning points

Bhandari

Mandal

2020

Indian Journal of Radiology and Imaging

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Dorsal agenesis of the pancreas is a rare entity, with about 100 cases reported. It can be overlooked on ultrasound due to the non visualization of the body and tail of the pancreas. This is due to overlying gas in the stomach, which offers a poor acoustic window and obscures visualization. Renal agenesis and Mullerian duct anomalies are uncommon associations of dorsal agenesis of the pancreas because of the separate embryological origin of the pancreas and genitourinary organs. Here, we present a case of a 17-year-old patient who had dorsal agenesis of the pancreas, associated with unilateral renal agenesis, unicornuate uterus, and ectopic ovary. We describe the anomalies and discuss the radiological differential diagnosis and potential pitfalls. We provide a brief review of the literature with few radiological teaching points and possible genetic implications of the case.

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Section: Discussionmentioning

confidence: 99%

A case of dorsal agenesis of pancreas associated with unilateral renal agenesis, unicornuate uterus, and ovarian ectopia: A brief review and learning points

Bhandari

Mandal

2020

Indian Journal of Radiology and Imaging

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“…A primary dysgenesis of the dorsal pancreatic bud and an ischemic insult to the developing pancreas are possible explanations. [ 1 ]…”

Section: Discussionmentioning

confidence: 99%

“…ADP was first described in 1911 in an autopsy study and was associated with diabetes mellitus. [ 1 ] Till now less than 100 cases of ADP have been reported in literature. [ 2 ] We report a case of incidentally detected ADP on Contrast Enhanced Computed Tomography (CECT) component of FDG PET/CT in a non-diabetic patient.…”

Section: Introductionmentioning

confidence: 99%

Incidentally detected agenesis of dorsal pancreas on pet/ct: Case report and review of literature

Kabnurkar¹,

Rokade²,

Bandekar³

et al. 2017

Indian J Nucl Med

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Agenesis of Dorsal Pancreas (ADP) is a rare congenital anomaly characterized by the absence of body and tail of pancreas. We report a case of incidentally detected ADP on Contrast Enhanced Computed Tomography (CECT) component of Fluorodeoxyglucose Positron Emission Tomography (FDG PET/CT) in a treated case of carcinoma (Ca) tongue with suspected local recurrence. Dependent Intestine Sign, hallmark of ADP on CECT imaging was noted in our patient.

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“…7 ADP is an extremely rare type of condition, and its prevalence remains unknown. 8 Pancreas development is a complex process and involves the fusion of two buds that grow from the foregut. The ventral bud gives rise to the most part of the head and uncinate process of the pancreas, while the dorsal bud gives rise to the cranial part of the head, body, and tail.…”

Section: Introductionmentioning

confidence: 99%

“…ADP is caused by lack of regression of the dorsal bud during embryonic development and can be complete or incomplete. 8,9 In the complete form, the accessory papilla, duct of Santorini, the body, and tail are missing. In the incomplete form, only the tail of the pancreas is absent.…”

Section: Introductionmentioning

confidence: 99%

Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report

Santana¹,

Abreu²,

Santos³

et al. 2021

BJOncology

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Solid pseudopapillary tumors (SPTs) of the pancreas are rare tumors with low potential for malignancy, uncertain lineage, and favorable prognosis in most cases. The SPT has an excellent prognosis, and the standard treatment is surgical resection. The agenesis of the dorsal pancreas (ADP) is an extremely rare type of congenital pancreatic malformation and is characterized by partial or total loss of the body and tail of the gland. Its association with SPT has been reported only in two studies. We report a case of SPT associated with total ADP. A 36-year-old woman was diagnosed with a complex mass on pancreatic head topography, measuring 7.8×5.5cm, associated with complete agenesis of the body and tail of the pancreas. She underwent gastropancreatoduodenectomy with a successful postoperative outcome. The anatomopathological examination suggested an SPT and it was confirmed by immunohistochemistry.

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Agenesis or pseudoagenesis of the dorsal pancreas

Abstract: The authors present an evidence-based case report of a patient with agenesis or pseudoagenesis of the dorsal pancreas.

Cited by 11 publications

References 8 publications

A case of dorsal agenesis of pancreas associated with unilateral renal agenesis, unicornuate uterus, and ovarian ectopia: A brief review and learning points

A case of dorsal agenesis of pancreas associated with unilateral renal agenesis, unicornuate uterus, and ovarian ectopia: A brief review and learning points

Incidentally detected agenesis of dorsal pancreas on pet/ct: Case report and review of literature

Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report

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