Solid pseudopapillary tumor associated with agenesis of the dorsal pancreas: a case report

Abstract

Solid pseudopapillary tumors (SPTs) of the pancreas are rare tumors with low potential for malignancy, uncertain lineage, and favorable prognosis in most cases. The SPT has an excellent prognosis, and the standard treatment is surgical resection. The agenesis of the dorsal pancreas (ADP) is an extremely rare type of congenital pancreatic malformation and is characterized by partial or total loss of the body and tail of the gland. Its association with SPT has been reported only in two studies. We report a case of SPT associated with total ADP. A 36-year-old woman was diagnosed with a complex mass on pancreatic head topography, measuring 7.8×5.5cm, associated with complete agenesis of the body and tail of the pancreas. She underwent gastropancreatoduodenectomy with a successful postoperative outcome. The anatomopathological examination suggested an SPT and it was confirmed by immunohistochemistry.

Pancreatic solid pseudopapillary neoplasm with concomitant left unilateral renal agenesis and bicornuate uterus: a case report

“…There have been occasional reports of SPN cases with pancreatic anomalies such as pancreatic dorsal agenesis 14 – 16 and pancreatic divisum 17 , 18 . There are instances of SPN being reported with familial adenomatous polyposis 19 , 20 .…”