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Micturition syncope: report of two cases Syncope is a symptom which is a transient loss of consciousness and very common in society and is one of the most important referral causes to emergency services. Micturition syncope (MS) appears as a rare cause of neurally-mediated syncope. MS is caused by reflex which results with vasodilatation and bradycardia, like defecation syncope. In the clinical setting, the MS is presented with transient loss of consciousness during.supine position or micturition following after a sleep period mostly iri otherwise healthy men. It is a reflex state in which standing triggers vasodilatation and bradicardia. MS covers 2-8% of all syncopes. There is still no consensus about treatment and outcome of MS. In this article two nriale patients with MS are presented. With these two cases, we aimed to give detailed information about micturition syncope which is a rare type of syncope. • ' ÖZETMiksiyon senkobu: iki olgu sunumu Toplumda sik gôrûlen ve acil servise baçvurunun önemli nedenlerinden olan senkop, kisa süreli geçici bilinç kaybi ile karakterizedir. Miksiyon senkobu (MS), nöral kôkenli refleks sendromlarindan birisidir. MS ve defekasyon senkobi^ vazodilatasyon ve bradikardi ile sonuçlanan refleks nedeniyle ortaya çikmaktadir. Klasik oiarak MS saglikli insenlarda, uykudan uyanip idrar yapma sonrasi geliçen senkop jeklinde tarif edilmektedir. Halen MS hakkindaki bilgiler çok sinirlidir. MS tum senkoplarin %2-8'ini oluçturmaktadir. MS'nin tedavi ve sonuçlan konusunda haleh görüc birligi yoktur. Sunacagimiz iki olgu ile nadir görülen bir senkop çeçidi olan miksiyon senkobuna ait aynntli bir degerlendimie yapilmasi amaçlanmiçtir. Anahtar kelimeler: Senkop, miksiyon senkobu, vazovagal refleks Address reprint requests to / Yaziçma adresi:

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Ad dress for Cor res pon den ce/Ya z›fl ma Ad re si: Ayşin Kısabay Ak MD,

Restless legs syndrome (RLS) is a disease characterized by some type of dysesthesia, an indescribable abnormal sensation in the extremities. Our objective was to determine whether the visual evoked potentials (VEP) can be used as a quantitative monitoring method to evaluate demyelination-remyelination and neurodegeneration in the patients with RLS. The present study was carried out prospectively. It was planned to determine normal or pathological conditions in the form of increased latency or decreased amplitude of VEP and to evaluate possible pathologies in the visual and retinal pathways at early stages and at months 3 and 6 of follow-up in the patients with RLS (with or without iron deficiency anemia), in those without RLS (at the time of diagnosis prior to any medical therapy) without any visual symptoms. It was observed that latency of VEP improved but didn't return to normal limits following treatment with dopamin agonists, iron, or combination of both and that there was no significant difference between the post-treatment data and those of the control group. These results in combination with the fact that the latencies and amplitudes didn't return to normal levels despite the 6-month-treatment but showed a progressive course with partial regeneration suggests that there was incomplete remyelination. It should be kept in mind that this syndrome is likely to be a part of neurodegenerative process.

Myasthenia gravis is a disease of neuromuscular junction due to auto-immune destruction of the acetylcholine receptors. Behçet's disease, on the other hand, is a multisystemic vascular-inflammatory disease. Both conditions are not common in the general population although their association has not been reported in the literature. We wanted to present our patient who developed clinical course of myasthenia gravis following discontinuation of medications due to complications of corticosteroid for Behçet's disease. It was observed that clinical findings of myasthenia gravis recovered following restarting steroid treatment and he did not experience attacks of both conditions. Although Myasthenia gravis and Behçet's disease are distinct entities clinically as well as in terms of pathogenesis, they share common physiopathological features and their treatment is based on their common features.

Öz Gaucher hastalığı, dalak karaciğer ve kemik iliğinde glukozilseramid birikimi ile karakterizedir. Hastalık otozomal resesif geçer ve lizozomal lipid depo hastalığıdır. Glukozilseramid hidrolaz (b-glukozidaz)'da genetik defekt sonucu retikuloendoteliyal sistem hücrelerinin lizozomlarda glukoseramid birikir. Gaucher hastalığında masif splenomegali ve sitopeniler görülür. 37 yaşında sitopeniler ve hepatosplenomegali nedeniyle hastanemize başvuran ve erişkin yaşta Gaucher hastalığı tanısı alan olgu sunuldu. Anahtar Sözcükler: Gaucher, sitopeni, splenomegali. Abstract Gaucher disease is characterized by the deposit of glucosylceramide in the spleen, liver and bone marrow. This lipid lysosomal storage disease shows autosomal recessive inheritance and. Glucosylceramide is stored in lysosomal bodies of the cells of the reticuloendothelial system as a result of a genetic defect in glucosylceramide hydrolase (b-glucosidase). Massive splenomegaly and cytopenias are seen in Gaucher disease. We presented a 37-year-old woman admitted to our hospital with cytopenias and splenomegaly and diagnosed as Gaucher disease in adult age.

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