<p class="Abstract">A 6 year old boy presented with sign symptoms of cerebral stroke. After clinical and radiological evaluation, a diagnosis of bilateral moyamoya disease was made. An indirect bypass surgery encephaloduroateriosynangiosis was done on the right side at first then on the left side. Patient was partially improved. At one year follow-up, there was the evidence of occlusion of collateral circulation on the right side and the patient became symptomatic again. It is noted that, although the early indirect bypass surgery is indicated in the pediatric patients for preventing the stroke but the outcome is difficult to judge.</p>
Hajdu-Cheney syndrome is an extremely rare genetic disorder of the connective tissue characterized by severe and excessive bone resorption leading to osteoporosis and a wide range of other potential symtromes. The clinical presentation and typical radiological features help in confirming the diagnosis. Hajdu-Cheney syndrome had not been reported previously in our country. Because of the rarity of the problem, we are interested to report a case of Hajdu-Cheney syndrome who was admitted in Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh. DOI: http://dx.doi.org/10.3329/bjch.v36i2.13086 Bangladesh J Child Health 2012; Vol 36 (2): 98-100
Blue rubber bleb nevus syndrome (BRBNS) is a rare condition that is characterized by malformations of the venous system that significantly involve the skin and viscera.Cutaneous malformations are usually asymptomatic and do not require treatment except cosmetic purpose. The treatment of gastrointestinal lesions is determined by the extent of involvement and severity of the disease.We are presenting a case of BRBNS who was admitted in the paediatric ward of Bangabandhu Sheikh Mujib Medical University(BSMMU) with the complaints of progressive pallor since one year of age, passage of blackish stool for last two years, presence of soft bluish/and swelling all over the body and multiple dark blue to blackish nodule present in palm and sole. She got blood transfusion over one hundred (100) times. Endoscopy showed multiple haemangioma with active bleeding in upper GIT. After possible investigations she was diagnosed as a case of BRBNS and treated with available treatment facility.Bangladesh J Child Health 2017; VOL 41 (2) :125-128
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