Relevance. Anatomical and functional disorders in congenital clefts may be various. Their severity depends on the cleft size and on the combination of a cleft lip with an alveolar cleft. Alveolar cleft bone grafting (ACBG) is one of the most important surgeries for patients with cleft lip and palate rehabilitation. The study aimed to analyze the results of alveolar cleft bone grafting in various age groups, summarizing the available data and supplementing them with our own experience.Materials and methods. In our clinic, 488 patients of different ages (from 4 to 18 years old), including patients with bilateral clefts, underwent ACBG.Results. The result analysis showed the time of surgery should depend not on the child's age but on the orthodontic preparation of the child for ACBG.Conclusion. The literature data and our experience allowed us to develop indications for ACBG at different ages
Relevance. Branchio-oto-renal syndrome (also known as Melnick-Fraser syndrome) is a rare syndrome characterized by hearing loss, renal malformations and branchial cyst (fistula) association. The article describes a clinical case of a boy with an atypical clinical picture of branchio-oto-renal syndrome.Material and methods. The patient was admitted to our clinic with acute inflammation, complaints of hearing loss and a fistulous tract in the right retromandibular region.Results. After the acute inflammation resolution and necessary investigations, the patient underwent a fistulectomy for diagnosis verification. We analyzed the patient routing from the first presentation to the patient's GP to the final diagnosis in our clinic. Based on this clinical case result analysis, we offered optimal diagnosis and treatment tactics for patients with Melnick-Fraser syndrome.Conclusion. Correct branchio-oto-renal syndrome diagnosis requires careful history taking, clinical examination and multidisciplinary team involvement. This approach will allow the patient to receive a full range of treatments with quality-of-life preservation.
Un cas rare d'aplasie pure des globules blancs chez un patient avec un thymome compliqué d'une endocardite infectieuseIntroduction. L'aplasie pure des globules blancs (PWCA) est une maladie hématologique rare caractérisée par l'absence de lignées de neutrophiles dans la moelle osseuse avec mégacaryopoïèse et érythropoïèse intactes. La PWCA est généralement associée à plusieurs pathologies immunitaires. La cytopénie chez les patients atteints de thymome est considérée comme l'une des maladies des syndromes paranéoplasiques avec d'autres manifestations. Les deux principaux problèmes cliniques de la PWCA sont diverses complications infectieuses et les lésions ulcéreuses-nécrotiques de la peau et des muqueuses. Rapport de cas. Cet article décrit le cas rare d'un patient atteint de thymome et de l'un de ses syndromes ABSTRACT Introduction. Pure white cell aplasia (PWCA) is a rare hematologic disorder characterized by the absence of neutrophil lineages in the bone marrow, with intact megakaryopoiesis and erythropoiesis. PWCA is commonly associated with several immune pathologies. Cytopenia in patients with thymoma is a paraneoplastic syndrome, along with other manifestations. The two major clinical issues in PWCA are various infectious complications and ulcerative-necrotic lesions of the skin and mucosa membranes. Case presentation. We present a rare case of a patient with thymoma and PWCA, as paraneoplastic syndrome. On the background of agranulocytosis, the patient developed sepsis and infective endocarditis (IE) caused by a rare agent, carbapenem-resistant Klebsiella pneumoniae.Conclusions. The rarity of endocarditis caused by Klebsiella species limits its recognition and awareness
РезюмеАктуальность. Одним из осложнений удаления зуба на верхней челюсти является интрузия зуба или корня зуба в верхнечелюстной синус (ВЧС) в связи с особенностями анатомии верхней челюсти и возможными техническими ошибками врача. Среди методов лечения чаще всего выбирают экстраназальные вмешательства, а именно радикальную синусотомию по Колдуэлл-Люку или пластику ороантрального сообщения с удалением инородного тела из ВЧС. Диагноз. В данной статье описаны два клинических случая. Оба пациента были госпитализированы в отделение детской челюстно-лицевой хирургии с диагнозом Инородное тело в верхнечелюстной пазухе. Представлен наш опыт эндоскопического удаления инородного тела из ВЧС у этих пациентов. Результаты. Методом лечения у данных пациентом было выбрано эндоскопическое удаление инородных тел из верхнечелюстной пазухи. Послеоперационный период проходил без особенностей и осложнений.
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