Kindler's syndrome (KS) is a rare inherited skin disease characterized by acral blistering, photosensitivity, progressive poikiloderma, and cutaneous atrophy along with different types of mucosal involvement. We hereby report KS in two siblings. The case is being reported for its rarity and for emphasizing the importance of considering this condition in the differential diagnosis of disorders that may cause blistering, cutaneous atrophy, and/or poikilodermatous skin changes. Besides, the presentation of the disease in two of the members of the same family makes the case even more interesting.
Lymphangioma circumscriptum is a rare disorder of lymphatic channels characterised by multiple grouped thin translucent vesicles. The lesions are often seen around the neck, upper trunk, proximal extremities and tongue. Genital involvement in females has been reported but penis is a rare site. On the other side congenital variety is extremely rare. Here we are presenting a rare case of congenital penile lymphangioma circumscriptum.
Lymphangioma circumscriptum is a rare disorder of lymphatic channels characterised by multiple grouped thin translucent vesicles. The lesions are often seen around the neck, upper trunk, proximal extremities and tongue. Genital involvement in females has been reported but penis is a rare site. On the other side congenital variety is extremely rare. Here we are presenting a rare case of congenital penile lymphangioma circumscriptum.
Langerhans cell histiocytosis (LCH), characterised by the infiltration of one or more organs by large mononuclear cells, may affect patients of any age but in adults the features of this disease is still poorly defined. Here, we report a case of an adult with crusted erosions in seborrheic distribution, Bilateral inguinal lymphadenopathy with ulceration, which on biopsy showed features of multisystem LCH, and was confirmed by immunohistochemistry. Despite chemotherapy and high dose antihistamines our patient complained of intractable pruritus which was relieved with Narrow Band UV-B phototherapy.
Despite achieving elimination of leprosy as a public health problem in 2005, India contributes to more than half the global burden of leprosy. Despite availability of accurate diagnostic techniques and effective therapy, such high numbers indicate inadequate and incorrect knowledge with widespread ignorance regarding leprosy.
METHODOLOGYA cross-sectional study was carried out among 300 patients attending the Dermatology Outpatient Department of our institute, selected by systematic random sampling from January 2014 to March 2014. Information regarding knowledge, attitudes and practices towards leprosy was obtained using a structured questionnaire.
RESULTAnalysis using Statistical Package for the Social Sciences, version 22 (SPSS v22) indicated that only 50% of respondents had knowledge about the disease. However, they were ignorant about the prominent symptoms and signs of the disease. Mis-information about the causes varied from food, unclean environment to impure blood; 70% of those interviewed knew that the disease can be treated by the drugs, but were unaware of the details and duration of treatment.
CONCLUSIONIn order to achieve the target of total eradication there is a need to intensify awareness about the symptoms of the disease, its treatment and prognosis so that early detection can be ensured.
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