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Background In the past 3 decades, the arterial switch procedure has replaced the atrial switch procedure as treatment of choice for transposition of the great arteries. Although survival is superior after the arterial switch procedure, data on pregnancy outcomes are scarce and transposition of the great arteries after arterial switch is not yet included in the modified World Health Organization classification of maternal cardiovascular risk. Methods and Results The ROPAC (Registry of Pregnancy and Cardiac disease) is an international prospective registry of pregnant women with cardiac disease, part of the European Society of Cardiology EURObservational Research Programme. Pregnancy outcomes in all women after an arterial switch procedure for transposition of the great arteries are described. The primary end point was a major adverse cardiovascular event, defined as combined end point of maternal death, supraventricular or ventricular arrhythmias requiring treatment, heart failure, aortic dissection, endocarditis, ischemic coronary events, and thromboembolic events. Altogether, 41 pregnant women (mean age, 26.7±3.9 years) were included, and there was no maternal mortality. A major adverse cardiovascular event occurred in 2 women (4.9%): heart failure in one (2.4%) and ventricular tachycardia in another (2.4%). One woman experienced fetal loss, whereas no neonatal mortality was observed. Conclusions Women after an arterial switch procedure for transposition of the great arteries tolerate pregnancy well, with a favorable maternal and fetal outcome. During counseling, most women should be reassured that the risk of pregnancy is low. Classification as modified World Health Organization risk class II seems appropriate.

We report the case of a 30-year old man who came to the emergency department of our hospital with acute left heart failure, and was diagnosed with a rare congenital anomaly (cor triatriatrum sinister), which can mimic a severe mitral stenosis. Cor triatriatum sinister is a rare anomaly (0.1% of all cases of congenital heart disease) that is seldom diagnosed in adult patients. The hallmark of this congenital defect is the presence of a fibromuscular membrane that divides the left atrium (LA) into two chambers: a postero-superior chamber into which the pulmonary veins drain and an infero-anterior chamber (true LA) containing the mitral valve and atrial appendage. Both chambers communicate through a membrane in which one or more drain holes can be found. When the hole is significantly obstructive, it results in increased venous and arterial pressures. Even though the definitive treatment of cor triatriatum is the surgical excision of the membrane, we present a balloon dilatation case with a good response to percutaneous therapy, both initially and in the ensuing months.Heart failure † Cor triatriatum sinister † Percutaneous repair Cor triatriatum sinister is a rare anomaly accounting for 0.1% of all cases of congenital heart disease. It is seldom diagnosed in adult patients. Case reportWe report a case of a 30-year-old male who presented to the Emergency Department complaining of fatigue, shortness of breath, and cough on exertion. The patient had been developing progressive symptoms over the past 6 weeks. During the past week the cough had worsened and he had also observed that expectoration was frequently stained with blood. His past medical history and family history were unremarkable. He worked as an information technology technician until he became ill.Shortly after arrival, the patient suffered a witnessed episode of large volume haemoptysis estimated to be . 250 mL of fresh blood. On physical examination, he appeared uncomfortable and in distress, and continued to cough up small amounts of blood. Vital signs were notable for a blood pressure of 101/60 mmHg, a regular pulse rate of 120 b.p.m., a respiratory rate of 36 breaths/ min, and an oxygen saturation of 93% on 100% oxygen via a highflow face mask. The cardiac exam demonstrated tachycardia, a normal S1, and an increased S2, probably in the context of pulmonary hypertension; however, the murmur was clearly diastolic, most probably in relation to the obstructive nature of the membrane.The lungs were notable for the presence of bilateral low-pitched rhonchi predominantly on the right side. Extremities were slightly cool, without cyanosis, clubbing, or oedema.The patient underwent immediate endotracheal intubation in order to secure the airway and was transferred to the Intensive Care Unit.The electrocardiogram showed sinus tachycardia and left atrial enlargement. Chest X-ray showed pulmonary artery enlargement and signs of venous hypertension. Transthoracic echocardiography (TTE) demonstrated the presence of a thin echo-bright membrane attached medially to ...

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