Background: teratomas is defined as germ cell tumors that derived from totipotent cells, some are entirely benign (mature) and some are malignant (immature) account for 80%, 3%, respectively. The majority of teratomas are found in gonads (ovary, testis) followed by extra-gonadal sites (sacrococcygeal, retroperitoneal, gastric, etc.). Aim of the study: this study aimed to report a rare cases of teratoma in Saudi Arabia. Method: this study was a case of a one-year old child with abdominal teratoma, which was discovered incidentally, and on reviewing the literature we found that only two cases of extragonadal abdominal teratomas reported from Saudi Arabia and this is the third one. Data were collected from patient's medical file after approval has been taken from bioethics department and the patient's family. Result: abdominal teratoma is rare and should be taken into consideration as one of the differential diagnosis of abdominal mass. Total excision is the mainstay of treatment. Conclusion: Abdominal teratoma is rare and should be taken into consideration as one of the differential diagnosis of abdominal mass, it is usually benign. Total excision is the mainstay of treatment. Careful histopathological examination and close follow-up is mandatory, only two cases were reported from Saudi Arabia and our case could be the third one.