Morquio syndrome is a rare autosomal recessive disorder of mucopolysaccharide metabolism, also called mucopolysaccharidosis type IV. We report a case of Morquio syndrome in a16-year- old girl of normal intelligence, who got herself admitted in Bangabandhu Sheikh Mujib Medical University, Dhaka, Bangladesh. The patient had short stature and skeletal deformity and she belonged to a non-consanguineous marriage of her parents. She was diagnosed on the basis of clinical features, typical radiological changes and positive urinary mucopolysaccharide screening test.Birdem Med J 2018; 8(3): 266-269
Aims: Vertigo is an abnormal perception of the movement of the environment or self and may result from diseases of the labyrinth, vestibular nerve or its central connections, vertebrobasilar insufficiency, and anxiety disorder. In this study, we aimed to evaluate the epidemiological and clinical characteristics of vertigo patients. Study Design: Descriptive cross-sectional study. Methodology: This cross-sectional study was done at the Neurology outpatient department (OPD) of Bangabandhu Sheikh Mujib Medical University (BSMMU) from September 2013 to August 2015. All the patients presenting with vertigo were evaluated by history, clinical examinations, Dix-Hallpike test, and appropriate investigations.
Background: Anton’s syndrome is a rare syndrome characterised by denial of blindness by a patient who obviously cannot see. Visual anosognosia and usually caused by bilateral occipital infarct. Rarely caused by demyelination or haemorrhage. Objective: The aim was to report a case of Anton’s syndrome due to bilateral occipito-parietal lobar haemorrhage following percutaneous coronary intervention due to myocardial infarction. Methods: The case was thoroughly evaluated clinically then diagnosis was confirmed by CT scan of head showing bilateral occipito-parietal haemorrhage. Result: The possible cause of bilateral lobar haemorrhage was due to use of Heparin during procedure and duel antiplatelet after percutaneous coronary intervention. Conclusion: A suspicion of cortical blindness and Anton’s syndrome should be raised in patients with atypical visual loss and evidence of bilateral occipital lobe injury. Though infarction is the common cause but any other cause that leads to bilateral occipital damage like haemorrhage in this patient may cause this syndrome. Drug induced extensive intracerabral haemorrhage is difficult to manage in the setting of myocardial infarction. Bangladesh Med Res Counc Bull 2021; 47(1): 98-100
No AbstractDOI: http://dx.doi.org/10.3329/uhj.v9i1.19515 University Heart Journal Vol. 9, No. 1, January 2013; 56-58
Background: The extent of damage by ischaemic stroke and the course of illness depend largely on the presence of collateral vessels around the affected area. The Circle of Willis (CoW), which serves as an important potential collateral pathway in maintaining adequate blood flow around the brain, is known to have variable patency. So the completeness of CoW is expected to influence the severity of ischaemic stroke. Objective: The objective of the study was to determine the association of completeness of Circle of Willis with severity of acute ischaemic stroke. Methods: It was a cross-sectional study done in Bangabandhu Sheikh Mujib Medical University, Dhaka from March, 2015 to August, 2017. A total of 42 patients of acute ischaemic stroke who were undergoing Digital Subtraction Angiography (DSA) for different reasons were selected by purposive sampling method. Data regarding completeness of Circle of Willis were obtained from DSA. National Institutes of Health Stroke Scale (NIHSS) score were measured to assess the severity of stroke. Then the severities of stroke between the complete and incomplete Circle of Willis groups were compared. Results: A total of 27 male and 15 female patients were enrolled. Among them, 47.6% (20) had complete CoW and it was incomplete in rest 52.4% (22). Median (range) of NIHSS scores of complete and incomplete CoW group was 4.5 (0-17) and 9.5 (3-21) respectively. Mean NIHSS (±SD) for the complete and incomplete CoW was 6.60 (±4.97) and 9.95 (±5.10) respectively. The difference of mean between the two groups was found to be statistically significant (p=0.037). Odd’s Ratio (OR) for development of more severe stroke in patients with incomplete CoW was 4.5, 95% Confidence Interval (CI) 1.18-18.13 which was statistically significant (p=0.029). Conclusion: It was concluded that incomplete Circle of Willis is associated with more severe stroke in acute ischaemic stroke patients. Bangladesh Med Res Counc Bull 2021; 47(2): 181-191
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