Being a rare clinical syndrome, Prune-Belly is a congenitally acquired disorder with a broad spectrum of abnormalities, ranging from incompatibility with life to ageing normally and having children of their own. This case series reports 2 different cases of Prune-Belly Syndrome being diagnosed in a short time frame from the same hospital with varied presentations. It also critically highlights the role of interprofessional team in managing with this complex condition.
Keywords: Prune-Belly, syndromic triad, multidisciplinary team approach
Undifferentiated endometrial sarcoma is a rare uterine malignancy of mesodermal origin. Only a few cases have been
reported in literature. Herein, we describe a 56-year old woman who presented with post-menopausal bleeding of a short
duration. Endometrial curettings were suggestive of undifferentiated sarcoma. Computed tomography showed an enlarged uterus with welldened mass in the endometrial cavity extending down to the cervix. A total abdominal hysterectomy, bilateral salpingo-oophorectomy, bilateral
pelvic and para-aortic lymphadenectomy and omental biopsies were taken. Histological examination revealed a tumour with a permeative growth
pattern composed of uniformly high grade round tumour cells with high mitotic activity. However, there was no lymphovascular space invasion.
Tumour cells were strongly positive for CD10 signifying high grade endometrial stromal sarcoma (HG-ESS). Post R0 resection, patient is now
receiving adjuvant chemotherapy. However, it is seen that most patients have early recurrence following even R0 resection.
Cervical descent is a major etiology of uterine prolapse. However, true elongation of cervix can cause uterine prolapse without its descent. Most patients find it difficult to come for follow-up visits to hospitals during the ongoing COVID surge. So, they prefer definitive surgeries. Moreover, young patients with prolapse want fertility preservation and subsequent pregnancies. So, we hereby report a case of Manchester operation being performed in a female with cervical elongation who was keen on uterus preservation, thereby analyzing the advantages of this procedure over conventional restorative surgeries for pelvic organ prolapse.
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