Este trabalho teve como objetivo apresentar os resultados obtidos na avaliação do processamento auditivo de um paciente com Neurofibromatose tipo 1. Embora a audição periférica estivesse normal nos testes realizados, foram observadas alterações importantes no processamento auditivo em várias habilidades. Este achado, descrito pela primeira vez na neurofibromatose, pode contribuir para explicar os distúrbios cognitivos e da aprendizagem já amplamente descritos nesta enfermidade genética comum.

structuralist analyses (e.g., Sten, 1944), a system of underlying oral vowels /i e ɛ a ɔ o u/ and another of underlying nasal vowels /ĩ ẽ ã õ ũ/ was proposed. Still in structuralist terms Câmara Jr. (1953;1970) proposed a double representation according to which nasality would spread leftwards to an underlying oral vowel from a tautosyllabic N. This N would then be deleted after [+nasal] spreading except when followed by a plosive, in which case an audible homorganic nasal consonant might be inserted. Thus, according to this double representation hypothesis, the Portuguese vowel system is to be restricted to oral vowels that become nasalized before a tautosyllabic N.The more surface-oriented proposal of two vowel systems is unable to cope with the distributional and phonological intricacies of nasalization. On the other hand, the double representation hypothesis, which proposes that they occur in heavy syllables, accounts well for the behaviour of Portuguese nasal vowels 2 . It is also in accordance with diachronic studies on the evolution of contrastive nasal vowels as VN > VÑ > Ṽ in Romance languages (Hajek, 1997;Sampson, 1999), a pattern also found in other unrelated languages such as Tibetan (Hogan, 1994) and Urdu (Naragan & Becker, 1971). Not surprisingly, the analysis of contrastive nasal vowels as VN sequences (henceforth VN analysis for short) was already proposed in generative terms as a universal nasalization rule (Lightner, 1970) before the first generative VN analysis for Portuguese vowels (Mateus, 1975). Since then, there has been no serious repudiation of the VN analyses, the proposal simply having been reinterpreted to accompany more recent theoretical frameworks.MW reinterpreted VN analysis in the autosegmental terms of CV phonology, whereby the nasal vowel becomes associated with a second time unit in the CV tier left by N after its deletion in the segmental tier. The association of a vowel with an extra time unit in the CV tier is the formal treatment of compensatory lengthening in CV phonology. Thus, it accounts for an important topic left unexplained by other VN analyses, the pervasive observation that nasal vowels are longer than their oral counterparts (Delattre, 1962;Delattre & Monnot, 1981; Beddor, 1993). It thus provides a phonological explanation of why in some languages nasal vowels often behave as long vowels. For instance, in Albanian Gheg nasal and long vowels never appear in unstressed position (Beci, 2006), and in Urdu, there are both long and short oral vowels, but short nasal vowels are rare (Naragan & Becker, 1971). On the other hand, it also requires that contextual or allophonic nasalization in Portuguese be explained by a different process than contrastive nasalization. Contextual nasalization affects a vowel before a heterosyllabic N, it is obligatory in stressed position or derived words (e.g. cama [ ̍ kɜmɐ] 'bed', cama+inha [kɜ ̍ mĩɲɐ] 'little bed') and optional otherwise (caminha [kɜ ̍ mĩɲɐ ~ ka ̍ mĩɲɐ] ~~~ On the duration of nasal vowels in brazilian portuguese Dia...