Primary mucosal malignant melanoma reported in this case is a rare clinical entity. Very few cases of primary mucosal malignant melanoma of middle ear have been reported in the literature till date. The etiopathology, clinical features and management of this disease has been described here.
We report a rare case of acquired localized cutis laxa in a teenage boy, without any preceding skin lesions. The area affected was the midface, extending to the chin, and involving the ears, leading to a prematurely aged appearance. Only five such cases have been previously published in the literature.
A solid variant of Aneurysmal Bone cyst is very rare tumour of maxilla. Histopathologically it is very much similar to giant cell granuloma but the radiographic features can influence the pathologic interpretation.A solid variant of anenurysmal bone cyst has been reported in facial bones and it can involve several adjacent bone synchronously (3). Both giant cell granuloma and aneurysmal bone cyst have a propensity for recurrence variably in the 15%-26% range (5).
Malignant nodular hidradenoma, also known as Malignant Hidradenocarcinoma (MHA), is a rare tumor of sweat glands that accounts for less than 0.001% of all tumors [1-3,14]. Although it typically arises de-novo, MHA rarely progresses from hidradenitis suppurativa (HS), a disorder of apocrine glands characterized by chronic inflammation [5,6,9]. HS is due to recurrent follicular occlusion leading to painful debilitating cutaneous/subcutaneous abscesses requiring drainage [5,6,9]. Common sites include axillary, anogenital and inguinal regions [5,6,9]. The worldwide prevalence of HS is 1%-4% [5,6]. Incidence of all eccrine carcinomas is ~ 6% [14]. Risk-factors include family history, obesity, and smoking [5,6,9]. Severe complications associated with HS are squamous cell carcinoma and adenocarcinoma [2,6]. MHA progression is extremely aggressive with 60% cases having metastatic spread within the first 2 years of diagnosis [14].
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