We describe a 4-year-old girl with anomalous origin of the left circumflex coronary artery from the right pulmonary artery and large atrial septal defect. This is the first reported case of such association. Surgical reimplantation of the anomalous left circumflex coronary artery to the aorta and atrial septal defect surgical closure was performed, with no postoperative complications.
Obstructed “total anomalous pulmonary venous connection” mostly presents with respiratory distress secondary to pulmonary congestion. We report two very sick patients who were referred to our cardiac center for intervention to relieve vertical vein (VV) obstruction. Due to hemodynamic instability and associated morbidity, the decision in our combined meeting was to go for interventional cardiac catheterization.
Highlights
Transcatheter occlusion of vertical vein in a partial anomalous pulmonary venous connection with dual drainage, case series with literature review.
In our manuscript we highlight the possibility of transcatheter Amplatzer device closure of PAPVD with dual drainage is an effective, safe and reproducible approach. It offers many advantages over surgical treatment such as fast recovery, avoidance of mechanical ventilation and PCICU stay, short in-hospital stay, low cost and more patient satisfaction.
In our series, it has been demonstrated that this approach showed appealing results, however larger scale studies and more follow-up periods are required to consolidate these findings.
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