Variations in Exstrophy of the Bladder

Marshall, Victor F.; Muecke, Edward C.

doi:10.1016/s0022-5347(17)64883-3

Cited by 190 publications

(49 citation statements)

References 67 publications

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“…The pseudoexstrophy is presence of characteristic muscular and skeletal defects of exstrophy without major defects in urinary tract as described by Marshall VF et al, 1962 [1]. The primary differentiating factor between covered exstrophy and pseudoexstrophy is that the former will generally have an ectopic bowel segment, commonly the colon present near the inferior abdominal wall [1,4,5]. A review of literature revealed 18 cases of pseudoexstrophy described till date, starting from 1954 by Hejtmancik et al [3].…”

Section: Discussionmentioning

confidence: 99%

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Pseudoexstrophy associated with penile duplication and hypospadias: A case report and literature review

Sandlas¹,

Jadh²

2018

j-pucr

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Bladder exstrophy is a rare developmental anomaly. Four principle variants of bladder exstrophy have been described and they themselves are rarer than the bladder exstrophy. Authors describe the management of a case of pseudoexstrophy type of variant in a 9 month old male child with penile duplication with torsion and coronal hypospadias. The rectal fascial defect was repaired without osteotomy as the distance between two pubic bones was <4 cm (3.1 cm). Genital reconstruction with excision of duplicate atrophic penile shaft and repair of coronal hypospadias with detorsion of the functional penile shaft could be accomplished. The patient had good outcome in terms of cosmesis and urinary stream. Total of 18 cases of the pseudoexstrophy have been described till date. Pseudoexstrophy of bladder is a very rare condition and can simultaneously present with other defects like omphalocele, anorectal malformations, pouch colon, multiple or solitary urogenital anomalies. The principles of correction though remain same with correction of abdominal wall defect with or without osteotomy depending upon severity of pubic diastasis. Other anomalies can undergo treatment as per standard protocol.

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Section: Discussionmentioning

confidence: 99%

“…Exstrophy of the bladder is a malformation that occurs in 1/25000 to 1/40000 births [1]. Four principle variants of bladder exstrophy have been described and they themselves are rarer than bladder exstrophy itself [2].…”

Section: Introductionmentioning

confidence: 99%

Pseudoexstrophy associated with penile duplication and hypospadias: A case report and literature review

Sandlas¹,

Jadh²

2018

j-pucr

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“…2 Several variants of classical bladder exstrophy have been described. 3 These include pseudoexstrophy in which the symphysis pubis is widened, but there is a normal anterior abdominal wall, bladder and urinary tract. Duplicate exstrophy is a variant in which the pelvic bones are also abnormal, the bladder is normal but there is a small piece of bladder mucosa on the anterior abdominal wall.…”

Section: Denouement and Discussionmentioning

confidence: 99%

Superior vesical fissure: variant classical bladder exstrophy

2007

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“…Exstrophy of the bladder is a rare anomaly with an incidence of 1 in 30,000-50,000 livebirths [1,2] . The variants of the exstrophy complex are much rarer and represent about 8% of the total cases [2] .…”

Section: Introductionmentioning

confidence: 99%

“…The variants of the exstrophy complex are much rarer and represent about 8% of the total cases [2] . Pseudoexstrophy is a rare variant of the exstrophy-epispadias complex, showing the musculoskeletal abnormalities of exstrophy without the urinary tract defects [1] .…”

Section: Introductionmentioning

confidence: 99%

Pseudoexstrophy with Epispadias

Mahajan

Ojha

Rao³

2005

Urol Int

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The exstrophy variants are uncommon anomalies. The variants of the exstrophy complex have all the stigmata of the classical exstrophy such as divergent recti, widened symphysis pubis, and low-set umbilicus; however, the urinary tract is intact to a varying degree. Pseudoexstrophy, an exstrophy variant, is very rarely associated with epispadias. We report an unusual case of pseudoexstrophy with epispadias, in whom the intact bladder was initially covered by a mucous membrane which later epithelialized. The epispadias was repaired using a penile disassembly technique with posterior and ventral placement of bladder neck and urethra. Although the urethral meatus was hypospadiac, the child had achieved dry intervals with occasional stress incontinence.

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Variations in Exstrophy of the Bladder

Cited by 190 publications

References 67 publications

Pseudoexstrophy associated with penile duplication and hypospadias: A case report and literature review

Pseudoexstrophy associated with penile duplication and hypospadias: A case report and literature review

Superior vesical fissure: variant classical bladder exstrophy

Pseudoexstrophy with Epispadias

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