Introduction: Transitional cell carcinoma (TCC) of the ovary is a rare and recently recognized variant of epithelial ovarian cancer. It has been described as primary ovarian carcinoma with definite urothelial features, without benign, metaplastic, and/or proliferating Brenner tumor (BT) identified.Case report: A 60-year-old lady presented with low back pain, growing abdominal mass, and loss of weight since 15 days. Magnetic resonance imaging (MRI) of abdomen showed a large ill-defined heterogeneous lesion with solid and cystic components. Beta human chorionic gonadotropin (β-hCG) and carcinoembryonic antigen (CEA) levels were raised. Surgery was performed and primary TCC of ovary was reported on histopathology.
Conclusion:Recognition of such tumors is important because of their rarity, favorable response to chemotherapy, and improved patient survival.