Syncopal Ventricular Tachycardia as the First Manifestation of Steinert's Disease

Arrhythmia-related workup in hereditary myopathies

“…6 Ventricular tachycardias may even be the initial manifestation of CI in the disease. 7 Severe arrhythmias like VTs or torsade de pointes may be particularly induced by hypokalemia with consecutive QT prolongation during general anesthesia. 8 In a study on 42 patients with MD1, 57% presented with electrocardiogram (ECG) abnormalities.…”