‘Swiss Cheese’ Lymphangiectasia in a Case of Solitary Morphea Profunda

Abstract

Reports of lymphangiectases that occur in lesions of morphea are rare. We describe a 24-year-old woman with a solitary morphea profunda associated with lymphangiectasia. Unlike previously reported cases, our case showed lymphatic dilatation resembling Swiss cheese and developed around a milium.

Three cases of bullous morphea: histopathologic findings with implications regarding pathogenesis

“…However, lymphatic obstruction with subsequent lymphangiectases is not the ultimate explanatory mechanism; although dilated lymphatic vessels are present in many reported cases of bullous morphea, they are not a constant finding . Moreover, cases of morphea with prominent lymphangiectases but with no bullous changes have been reported . None of the patients in our cases presented with lymphangiectases.…”

“…2,4 Moreover, cases of morphea with prominent lymphangiectases but with no bullous changes have been reported. 5 None of the patients in our cases presented with lymphangiectases. In one case (case 1) we studied the biopsy with D2-40 and showed how the lymphatics were flattened rather than distended and dilated.…”

“…Moreover, there are reports of morphea cases with prominent lymphangiectases in which bullae have not developed. 5 We describe three cases of bullous morphea in which no lymphangiectases were present.…”

“…However, not all published cases of bullous morphea have shown associated lymphangiectases. Moreover, there are reports of morphea cases with prominent lymphangiectases in which bullae have not developed …”

Morfea profunda solitaria. Una forma infrecuente de esclerodermia localizada en la infancia. Caso clínico

“…10 Otros hallazgos descritos han sido la coexistencia de osteoma cutis, así como la presencia de mucina, múltiples linfangiectasias y quistes de millium. 4,11,12 A u n q u e e l d i a g n ó s t i c o d e l a M P S e s predominantemente clínico-histológico, la ecografía cutánea es una técnica no invasiva, rápida y de bajo costo que puede ser útil en el diagnóstico y en el seguimiento de esta entidad, sobre todo, en la edad pediátrica. 13 Los hallazgos ecográficos pueden ser inespecíficos;…”