Surgical resection of right ventricular rhabdomyoma under the guidance of transesophageal echocardiography on a beating heart

Han, Xueguang; Song, Haibo; Zhou, Li; Jiang, Chunling

doi:10.21037/jtd.2017.02.63

Cited by 5 publications

(4 citation statements)

References 18 publications

Supporting

Mentioning

Contrasting

Unclassified

Order By: Relevance

“…Опыт хирургического лечения рабдомиом сердца в периоде новорожденности ограничивается единичными наблюдениями в связи с высокой частотой спонтанной регрессии опухоли [18,19,20]. В случаях, подобных нашему, выраженная обструкция выходного отдела правого желудочка может привести к жизнеугрожающим нарушениям гемодинамики, что не позволяет выбрать консервативную тактику наблюдения в надежде на спонтанный регресс опухоли [21,22,23]. Локализация новообразования в области выводного тракта правого желудочка обеспечила хороший хирургический доступ и полное удаление опухоли из небольшой вентрикулотомии.…”

Section: Discussionunclassified

Successful surgery for a right ventricle rhabdomyoma in a neonate

et al. 2020

View full text Add to dashboard Cite

Primary cardiac tumors are very rare in children. Rhabdomyoma is the most common benign tumor in fetuses and neonates. Most cases do not require any surgical intervention due to absence of clinical symptoms and a high rate of spontaneous regression within the first year of life. However, some neonates can have significant abnormalities of intracardial hemodynamics related to the obstruction of the left and right ventricle outflows; this is an indication to emergency surgery. As a rule, complete or partial resection of the tumor mass provides uneventful postoperative course and is not associated with a relapse of rhabdomyoma in the long-term.We present a clinical case of a 15-days old neonate who underwent an emergency surgery due to advanced tumor obstruction of the blood flow in the right ventricle outflow tract (RVOT). At preoperative echocardiography, there was a pulmonary artery systolic pressure gradient of 90 mm Hg. Moderate hypoxemia (SaO2 90%), breathing rate of up to 55 per minute, together with echocardiographic results, indicated the impaired pulmonary blood flow and the need for the tumor resection. The tumor was completely resected through the right ventricle access with cardiopulmonary bypass and cardioplegia, with subsequent autologous pericardium patching of the right ventricle. The postoperative period was uneventful; the patient was extubated at day 2 and discharged at day 11 after surgery. The diagnosis of rhabdomyoma was confirmed histologically. At one month after surgery, no additional tumor masses were found in the heart chambers and septum.Rhabdomyoma causing severe obstruction of the RVOT in a newborn is a rare life-threatening complication of the natural course of benign heart tumors in children. The presence of dyspnea at rest, moderate desaturation, and echocardiographic data determined the rejection of the conservative management commonly adopted in most cases of cardiac rhabdomyomas, and were indications for an emergency surgery. In the long-term postoperative period, magnetic resonance imaging should be done to exclude tuberous sclerosis.

show abstract

Section: Discussionunclassified

Successful surgery for a right ventricle rhabdomyoma in a neonate

et al. 2020

View full text Add to dashboard Cite

show abstract

“…According to the literature, it is also possible to take a chance on surgical resection of growing fetal cardiac tumour [25][26][27][28].…”

Section: Discussionmentioning

confidence: 99%

Fetal cardiac tumours in a referral prenatal cardiology centre – series of 37 cases with neonatal follow-up

Strzelecka¹,

Sylwestrzak²,

Krekora³

et al. 2019

pcard

View full text Add to dashboard Cite

Introduction: Fetal cardiac tumours are relatively rare findings. The aim of this research was to present the natural course in a series of 37 fetuses with cardiac tumours, who had fetal echocardiography performed and the pregnancies had been continued until term. Material and methods: This was a retrospective analysis of 37 cases with prenatally detected heart tumour. The study group was divided into multiple-and single-tumour subgroups and into survivors versus non-survivors. The number of survivors in subgroups and the incidence of prognostic factors were compared by c 2 test. The presence of additional cardiac anomalies, the way of delivery and neonatal follow-up was analysed. The literature (Pub Med) was reviewed. Results: There was no statistical difference between the number of survivors in groups of single versus multiple tumours (p > 0.05). In group of non-survivors there was a higher incidence of bad prognostic factors detected prenatally: pericardial effusion, mitral regurgitation, and cardiomegaly (p < 0.05). The authors suggested a different way of perinatal care and counselling in multiple and single fetal heart tumours. Conclusions: Fetal cardiac tumours in the majority of cases were rhabdomyoma, and in case of normal heart anatomy and normal intracardiac flow the short-term prognosis was good. Fetal single heart tumour with progression of its size in the third trimester may require early surgical resection, so delivery in a tertiary perinatal and cardiac surgery centre might be necessary. Pericardial effusion, mitral regurgitation, and cardiomegaly might implicate a worse prognosis in the case of fetal heart tumour. Fetal cardiac tumour may require a multispecialist team approach to benefit from early detection and diagnosis.

show abstract

“…As the improvement of monitoring conditions, TEE, offers better sound transmission and more windows which allows perioperative team to detect more valuable information compared with TTE, is widely used as a diagnostic and real-time monitoring tool [8]. The utility of intraoperative TEE is able to identify new pathologic findings and assess surgery procedure, consequently, influence surgi-cal decisions and provide the basis for perioperative team to make medicines, fluid managements, etc.…”

Section: Discussionmentioning

confidence: 99%

“…Presently, transesophageal echocardiography (TEE) is frequently used intraoperative for it's able to identify new pathologic findings, assess surgery procedure and potentially influence surgical decisions [8].…”

Section: Introductionmentioning

confidence: 99%

TEE Provided Advantageous Information for a Surgical Resolution of Obstruction of SAS Suffering Difficulty in Removing CPB: A Case Report

Lin¹,

Chen

Zhou

et al. 2019

BJSTR

View full text Add to dashboard Cite

Congenital heart disease (CHD) is the most common type of congenital malformations. Congenital supravalvular aortic stenosis (SAS), one kind of CHDs, is strongly associated with abnormal aortic sac development with low prevalence while shows considerable impacts on infants' physical and mental development. Presently, surgical treatment is an effective therapy for SAS with acceptable surgical risk and good late survival. Evaluating the stenosis grade preoperative, the real-time status of heart during surgical correction are extremely crucial. Transesophageal echocardiography (TEE), has the advantages of clear images without interference of surgical field, is widely applied in diagnosis of cardiovascular diseases and intraoperative continuously monitoring. Here, we presented a successful case of surgical resolution of obstruction of congenital SAS in an infant who suffered difficulties in removing cardiopulmonary bypass (CPB) under the guidance of TEE.

show abstract

Surgical resection of right ventricular rhabdomyoma under the guidance of transesophageal echocardiography on a beating heart

Cited by 5 publications

References 18 publications

Successful surgery for a right ventricle rhabdomyoma in a neonate

Successful surgery for a right ventricle rhabdomyoma in a neonate

Fetal cardiac tumours in a referral prenatal cardiology centre – series of 37 cases with neonatal follow-up

TEE Provided Advantageous Information for a Surgical Resolution of Obstruction of SAS Suffering Difficulty in Removing CPB: A Case Report

Contact Info

Product

Resources

About