Surgical Correction of Truncus Arteriosus With Unusual Origin of the Right Coronary Artery

Rodriguez, Humberto; Montero, Hernán; Fernandez, A.; Guzman, Armando; Sessa, T

doi:10.1177/2150135115596585

Cited by 3 publications

(1 citation statement)

References 4 publications

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“…Coronary artery is usually normal; rarely coronary artery course anomalies are seen. The single coronary artery and an intramural course as the most important variations 9 . Ventricular septal defect is classically subarterial in 80% of the cases.…”

Section: Discussionmentioning

confidence: 99%

Truncus arteriosus with double aortic arch: A rare association

Yıldırım

2017

Turk J Pediatr

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Truncus arteriosus (TA) is a congenital heart defect often diagnosed in neonatal period; it represents 0.7% of all congenital heart lesions. The pulmonary arteries originate generally above the coronary ostium. Aorto-pulmonary and interventricular defects are believed to represent an abnormality of conotruncal septation. TA is classified into four types, according to Van Praagh and Colette Edwards. Some of congenital heart defects may be associated with TA, such as aortic interruption. In literature, TA with a double aortic arch is observed as a very rare condition. We present here a newborn diagnosed with a combination of TA type 1 and double aortic arch.

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Section: Discussionmentioning

confidence: 99%

Truncus arteriosus with double aortic arch: A rare association

Yıldırım

2017

Turk J Pediatr

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Congenital Heart Disease Patterns

Richardson

2019

Atlas of Pediatric CTA of Coronary Artery Anomalies

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Anomalous Fusion of Right Pulmonary Artery to Aortic Arch: Case Report of a Rare and Fatal Congenital Malformation in a Newborn and a Literature Review

et al. 2018

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Patient: Female, newbornFinal Diagnosis: Anomalous fusion of right pulmonary artery-to-aortic archSymptoms: Respiratory failureMedication: —Clinical Procedure: —Specialty: CardiologyObjective:Congenital defects/diseasesBackground:We present a report of a rare cardiac malformation case as well as a review of the literature. In addition, the diagnostic features are discussed.Case Report:The case of a female newborn who died on her third day of life was studied at the Institute of Legal Medicine, University of Chieti-Pescara (Italy). The investigations around her death revealed a cardiac congenital malformation, seen as a rare variant of a common arterial trunk, in which the aorta was fused with the right branch of the pulmonary artery. The ascending aorta showed hypoplasia, while the coronary arteries were free of any pathological findings. The atrial septum showed a closed foramen ovale and the ventricular septum did not show any defect. Only an isolated right ventricular hypertrophy and dilation with no other cardiac abnormalities was found. The cause of death was acute respiratory failure on the third day of extrauterine life when the ductus Botalli closed. The karyotype analysis performed in this case was normal, and the fluorescent in situ hybridization analysis did not show the 22q11.2 microdeletion suggestive of the DiGeorge syndrome.Conclusions:These findings underline the value of 3-dimensional/4-dimensional ultrasound imaging when added to a fetal cardiology screening program, and the need for improvements in postnatal screening routines by using pulse oximetry in order to discover isolated vascular defects before circulatory collapse occurs, as well as to reduce the medico-legal disputes in cases of missed diagnosis. We found the relevant literature search lacked a description of this congenital malformation, which supports our deeper perinatal investigation.

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Surgical Correction of Truncus Arteriosus With Unusual Origin of the Right Coronary Artery

Cited by 3 publications

References 4 publications

Truncus arteriosus with double aortic arch: A rare association

Truncus arteriosus with double aortic arch: A rare association

Congenital Heart Disease Patterns

Anomalous Fusion of Right Pulmonary Artery to Aortic Arch: Case Report of a Rare and Fatal Congenital Malformation in a Newborn and a Literature Review

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