Supernumerary Nostril with Congenital Cataract

Abstract

Supernumerary nostril is a ve,y rare congenital anomaly. It can be unilateral or bilateral, and it sometimes occurs in the pres ence of other congenital deformities. Behind the external opening ofa supernumerary nostril is a small accessory nasal cavity, which mayor may not communicate with the normal nasal cavity on the same side. We describe a new case in which the supernumerary nostril with a small accessory nasal cavity, which did not communicate with the normal nasal cavity on the same side, appeared in a young girl who also had microcornea and congenital cataract. The accessory nasal cavity was successfu lly removed surgically. We believe that this case may represent thefirst reported case ofa supernumerary nostril with a congenital cataract on the same side. We also discuss the hypotheses that have been proposed to explain supe rnumerary nostrils.

Supernumerary Nostril: A Case Report and Review

“…Reddy & Rao (1987) reported a case of a third nostril that was situated below the left nostril. Sinha et al (2005) described a case of supernumerary nostril with micro cornea and congenital cataract.…”

Congenital hydrocephalus, corpus callosum agenesis, and prosencephalic cyst with supernumerary nostril: A neurocristopathy

“…Associated congenital deformities are seen in 45% of the patients, among them craniofacial malformations are the most common. [ 2 7 ] Reported anomalies are incomplete facial cleft,[ 8 ] ipsilateral congenital cataract and microcornea,[ 9 ] congenital double columella,[ 2 ] patent ductus arteriosus, central incisor fusion, severe sensorineural deafness,[ 10 ] ipsilateral/contralateral naso-ocular cleft, cleft palate and lip, hypoplastic heminose, congenital auricular hypoplasia, esophageal atresia, imperforate anus, frontonasal dysplasia,[ 2 ] dermoid cyst at the contralateral nasomaxillary groove,[ 2 ] and congenital adrenal hyperplasia with clitoromegaly. [ 11 ] Furthermore, anophthalmia of the contralateral eye with multiple hemangiomas of head and chest have been reported.…”

Supernumerary nostril: Congenital adrenal hyperplasia with a rare congenital anomaly

“…A case associated with microcornea was reported in 2005 and another one together with esophagus atresia, imperforated anus and PDA was reported in 2009. [ 1 2 3 4 5 ] Several cases, which are not connected with the unilateral nasal cavity have also been reported. Duplication anomalies of the nose include polyhinia and supernumerary nostril.…”

“…They are also reported with other congenital malformations such as facial clefts and congenital anomalies like congenital auricular hypoplasia, congenital cataracts, esophageal atresia and patent ductus arteriosus (PDA). [ 2 3 ] No case of an supernumerary nostril and congenital adrenal hyperplasia co-existence has been reported previously in English literature. Here, we report a case of supernumerary nostril with congenital adrenal hyperplasia.…”