Successful One-Stage Complete Removal of an Entire Intravenous Leiomyomatosis in the Heart, Vena Cava, and Uterus

A Giant Uterine Vascular Leiomyomatosis; A Rare Cause of Menometrorrhagia

“…13 Arinami et al reported that more appropriate results could be provided in the extraction of intra-cardiac extended or intravenously invaded cases, of both primary tumour and these extensions at the same session with cardiopulmonary by-pass. 14 Since the tumour is hormone-dependent and for this reason, there is the probability of increase of recurrence, salpingo-oophorectomy can be added to the operation in appropriate cases. According to the literature, the follow up of these cases should be long.…”

“…According to the literature, the follow up of these cases should be long. 1,14 The cases should be followed-up with ultrasound or magnetic resonance methods in the post-operative period periodically in order to detect recurrence or residual tumour. 13 It is especially highly typical to see a mass in the inferior vena cava and the heart on magnetic resonance imaging.…”

Surgical treatment of intracardiac leiomyomatosis

“…20 Otherwise, single-stage resection under the support of DHCA could proceed with success. 11,[21][22][23] As a simple and safe approach to removing the iliocaval portion of the IVL, iliac venotomy could be used in 1-and 2-stage operations. 24 Surgical mortality is low, and the follow-up study in our series suggests that the recurrence rate is also low.…”

Echocardiographic Characteristics of Intravenous Leiomyomatosis with Intracardiac Extension: A Single-Institution Experience

“…The clinical characteristics of these patients were consistent with the results of prior case studies. The most common symptoms were exertional dyspnea and palpition though the spectrum of symptoms were quite variable, including sudden death, syncope, cardiac tamponade, arrhythmias, abdominal abnormal bleeding, and massive ascites 8 . According to literature, more than half (57.1%) of patients had a hysterectomy and the median interval between the hysterectomy and the diagnosis of IVL with cardiac involvement was 4 years 3 .…”

“…The most common symptoms were exertional dyspnea and palpition though the spectrum of symptoms were quite variable, including sudden death, syncope, cardiac tamponade, arrhythmias, abdominal ab-normal bleeding, and massive ascites. 8 According to literature, more than half (57.1%) of patients had a hysterectomy and the median interval between the hysterectomy and the diagnosis of IVL with cardiac involvement was 4 years. 3 In the present study, 70% patients had a hysterectomy with diagnosis of hysteromyoma and the median interval was 3.4 years, which illustrate the silent and slow-growing characteristics of this benign smooth muscle tumor with semimalignant behavior.…”