Sturge-Weber syndrome with pyogenic granuloma

Mopagar, Viddyasagar; Choudhari, Shantanu; Subbaraya, Dwijendra Kocherlakota; Peesapati, Sudha

doi:10.4103/0976-237x.118345

Cited by 4 publications

(2 citation statements)

References 6 publications

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“…Moreover, PG case reported in patient with Sturge-Weber Syndrome (SWS), or Encephalotrigeminal angiomatosis. This syndrome is responsible for gingival enlargement, because of increasing the vascular component, and the additional local irritation by plaque and calculus act as the "perfect combination" for the PG [13].…”

Section: Methodsmentioning

confidence: 99%

Pyogenic Granuloma: A Literature Review and A Case Report

Georgoulis

Zarenti

Anastasopoulos

et al. 2022

EJDENT

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Pyogenic granuloma of the oral cavity is a common, non-neoplastic, vascular tumor. The etiology is not clear and it is suggested to be attributed to different factors. It might be caused by a reaction to a stimulus such as trauma, viruses such as HSV-1, hormonal changes, as well as other factors such as tooth eruption or medication. Clinically it appears as a painless tumor that tends to bleed easily, with red color and rarely may be accompanied by a periodontal abscess and bone loss. Biopsy is the most common tool used for the diagnosis. Its treatment is usually surgical excision and lately the use of lasers for its excision has emerged. Special care should be given to pregnant women where the treatment varies. The aim of this review is to present the background of oral pyogenic granuloma and the case report presents the situation, histological image and treatment of an adult woman patient.

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Section: Methodsmentioning

confidence: 99%

Pyogenic Granuloma: A Literature Review and A Case Report

Georgoulis

Zarenti

Anastasopoulos

et al. 2022

EJDENT

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“…This may arise within capillary malformation both in the skin and mucosa. 36,37 In some instances, these "angiomatous" nodules show a well-circumscribed proliferation of thick-walled muscle-containing blood vessels, lined by a single layer of endothelial cells resembling arteries, but lacking a well-formed elastic internal membrane and have been named acral arteriovenous tumors. 38 It has been proposed that they can spontaneously grow from abnormal and microscopic arteriovenous anastomoses within the context of ectatic capillaries and veins.…”

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confidence: 99%

Sturge-Weber Syndrome: A Review of Pathophysiology, Genetics, Clinical Features, and Current Management Approache

Sanchez-Espino¹,

Ivars²,

Antoñanzas³

et al. 2023

TACG

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Sturge-Weber syndrome (SWS) is a congenital, sporadic, and rare neurocutaneous disorder, characterized by the presence of a facial port-wine birthmark (PWB), glaucoma, and neurological manifestations including leptomeningeal angiomatosis and seizures. It is caused by a postzygotic, somatic, gain-of-function variant of the GNAQ gene, and more recently, the GNA11 gene in association with distinctive clinical features. Neuroimaging can help identify and stratify patients at risk for significant complications allowing closer follow-up; although no presymptomatic treatment has been demonstrated to be effective to date, these patients could benefit from early treatment and/or supportive interventions. Choroid plexus (CP) thickness measurements in brain magnetic resonance imaging (MRI) have a high sensitivity and specificity for early and incipient changes in SWS. In contrast, the absence of pathologic findings makes it possible to rule out associated neurological involvement and leads to periodical observation, with new imaging studies only in cases of new clinical signs/symptoms. Periodic ophthalmological examination is also recommended every 3 months during the first year and yearly afterwards to monitor for glaucoma and choroidal hemangiomas. Treatment for SWS depends on the extent and areas that are affected. These include laser surgery for PWB, anticonvulsants in the case of brain involvement, with either seizures or abnormal EEG, and medical treatment or surgery for glaucoma. Sirolimus has been used in a limited number of patients and appears to be a safe and potentially effective treatment for cutaneous and extra-cutaneous features, however controlled clinical studies have not been carried out. Better knowledge of GNAQ/GNA11 molecular pathways will help to develop future targeted treatments.

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Lobular Capillary Haemangioma of the Oral Cavity in a 11-Year-Old Child - A Case Report

Phadnis¹

2021

jemds

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Lobular capillary haemangiomas are benign vascular neoplasms that typically affect the skin or mucous membrane. Majority of the cases reporting lobular capillary haemangioma commonly involve the gingiva. There are rare cases presenting involvement of other parts of the oral cavity like buccal mucosa. The management of vascular lesions is more complex in children due to fear of uncontrollable bleeding. The case presented here reports a successful management of lobular capillary haemangioma of the buccal mucosa in an 11 - year - old child. Vascular lesions are one of the rare disorders affecting the overall quality of life of a child. American Academy of Paediatric Dentistry (AAPD) has presented numerous lesions, masses, or tumour-like conditions of hard and soft tissues within the oral and maxillofacial regions of children and young adults; most of these lesions being mucosal conditions. Oral vascular tumours encompass a wide spectrum of anomalies in children. In spite of the fact that a few cases are congenital, most of them arise during childhood.1 The vascular lesions of childhood are classified into two categories: haemangiomas (proliferating or involuting) and vascular malformations. Haemangioma is a term that envelops a heterogeneous gathering of clinical benign vascular lesions that share similar histologic features and presents as a proliferating mass of blood vessels. Haemangiomas are classified on the basis of their histological1 appearance as capillary, mixed or cavernous haemangiomas depending on the size of the vascular spaces or a sclerosing variety that tends to undergo fibrosis. Capillary haemangiomas are of two types; lobular capillary haemangioma and non-lobular capillary haemangioma depending on their histological features. Lobular capillary haemangioma (LCH) is a common reactive angiomatous proliferation of skin and mucous membranes.2,3 LCH (Mills et al. 1980 ) represents an essential, underlying lesion of pyogenic granuloma (PG).4,5 Based on the available literature and case reports, several clinical and histological differences were seen between PG and LCH, yet there is no clear distinction between the two and still remains a topic of debate. The peak prevalence of LCH is in paediatric population and young adults, with a female predilection. Although LCH is one of the most common soft tissue tumours of head and neck accounting for almost 6 % of all cases, there is a striking predilection for lesions on the gingiva. The occurrence of intraoral haemangiomas at sites such as lips, tongue, buccal mucosa, and palate are extremely rare. LCH is a tumour-like growth of the oral cavity or skin that is considered to be non-neoplastic in nature. The purpose of this paper is to report a case of lobular capillary haemangioma in a paediatric patient and describe the successful treatment of this case.

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Sturge-Weber syndrome with pyogenic granuloma

Cited by 4 publications

References 6 publications

Pyogenic Granuloma: A Literature Review and A Case Report

Pyogenic Granuloma: A Literature Review and A Case Report

Sturge-Weber Syndrome: A Review of Pathophysiology, Genetics, Clinical Features, and Current Management Approache

Lobular Capillary Haemangioma of the Oral Cavity in a 11-Year-Old Child - A Case Report

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