Stielgedrehtes, intraabdominales Lymphangiom

Intraabdominal Cystic Lymphangiomas in Children: A Single Center Experience

“…Misleadingly, mesenterial cysts and ICL are often classified together. The differentiation between these two types of cysts, however, is of prognostic relevance due to a recurrence risk in case of incomplete resection of an ICL [1,3,13,14]. Due to an adverse anatomic localization, incompletely removed ICL often results in a progressive, infiltrative growth in the relapse phase, and this might also require the additional removal of the involved intestinal or organ segments [9].…”

“…An intraabdominal location of cystic lymphangiomas can be shown in 5% of all lymphangiomas corresponding to an incidence between 1:27,000 and 1:250,000 [1]. Generally, this type of lymphangioma is detected in the first decade of life, and in 60% of the cases it is diagnosed even before the fifth year of life with a significant male predominance [1,[3][4][5]. Clinical signs are often unspecific depending on size and location of the process ranging from acute abdominal symptoms, via chronic abdominal pain to an accidentally detected space-occupying lesion or intraabdominal fluid accumulation in asymptomatic patients [2,3,6].…”

“…Intraabdominal cystic lymphangiomas (ICLs) are congenital malformations of extended lymphatic vessels whose connection to the venous and lymphatic system are supposed to be defective [1,2]. An intraabdominal location of cystic lymphangiomas can be shown in 5% of all lymphangiomas corresponding to an incidence between 1:27,000 and 1:250,000 [1].…”

“…Intraabdominal cystic lymphangiomas (ICLs) are congenital malformations of extended lymphatic vessels whose connection to the venous and lymphatic system are supposed to be defective [1,2]. An intraabdominal location of cystic lymphangiomas can be shown in 5% of all lymphangiomas corresponding to an incidence between 1:27,000 and 1:250,000 [1]. Generally, this type of lymphangioma is detected in the first decade of life, and in 60% of the cases it is diagnosed even before the fifth year of life with a significant male predominance [1,[3][4][5].…”

“…Even though ICL can cause acute abdominal symptoms through bowel obstruction, inflammation or intracystic hemorrhage, most of the patients present with unspecific abdominal signs like nausea, vomiting, diarrhea, constipation, palpable abdominal mass, increasing abdominal girth, digestive disorders, melena or pseudo-ascites. Only a minority of ICLs are asymptomatic and detected incidentally [1][2][3]6]. Due to the multitude of symptoms diagnosis can be challenging [7].…”